[Acute mucocutaneous lymph node syndrome (Kawasaki-syndrome) with fatal periarteritis nodosa of the coronary arteries. Another case from Europe].
Case report of a 1 8/12-year-old boy suffering from an acute febrile disease with phlegmonous cervical lymphadenopathy, skin rash and other septic symptoms. Bacterial cultures were sterile, and antibiotics had no effect, whereas prednisone made an immediate improvement. On the 23rd day of illness the patient died unexpectedly. Autopsy revealed a ruptured coronary aneurysm due to periarteritis nodosa. This curious disease of yet unknown cause is quite frequent in Japan, but very rare in Europe.
D001013:Aorta, Thoracic; D001014:Aortic Aneurysm / Q000209:etiology; D001019:Aortic Rupture / Q000209:etiology; D006801:Humans; D007223:Infant; D008206:Lymphatic Diseases / Q000150:complications*; D008297:Male; D009080:Mucocutaneous Lymph Node Syndrome / Q000150:complications* / Q000188:drug therapy; D010488:Polyarteritis Nodosa / Q000150:complications*; D011241:Prednisone / Q000627:therapeutic use
D011241:Prednisone
Akutes mukokutanes Lymphknotensyndrom (Kawasaki-Syndrom) mit letaler Periarteriitis nodosa der Kranzarterien. Ein weierer Fall aus Europa.