The gamma-glutamyl cycle and amino acid transport. Studies of free amino acids, gamma-glutamyl-cysteine and glutathione in erythrocytes from patients with 5-oxoprolinuria (glutathione synthetase deficiency).
D000328:Adult; D000596:Amino Acids / Q000097:blood* / Q000378:metabolism; D001692:Biological Transport; D002648:Child; D002675:Child, Preschool; D004151:Dipeptides / Q000097:blood*; D004912:Erythrocytes / Q000032:analysis*; D005260:Female; D005721:Glutamate-Cysteine Ligase / Q000378:metabolism; D005978:Glutathione / Q000097:blood*; D005981:Glutathione Synthase / Q000172:deficiency*; D006801:Humans; D010453:Peptide Synthases / Q000172:deficiency*; D011760:Pyrrolidinones / Q000652:urine*; D011761:Pyrrolidonecarboxylic Acid / Q000652:urine*
D000596:Amino Acids; D004151:Dipeptides; D011760:Pyrrolidinones; D010453:Peptide Synthases; D005721:Glutamate-Cysteine Ligase; D005981:Glutathione Synthase; D005978:Glutathione; D011761:Pyrrolidonecarboxylic Acid