[Histological and ultrastructural study of intestinal ganglioneuromatosis. The multiple endocrine neoplasms type IIb syndrome].
The syndrome known as the Multiple Endocrine Neoplasia type III or type IIb presents a particular histological intestinal lesion: hyperplasia of the myenteric plexus. The electron microscopic study of the plexus of Auerbach in our observation suggests a disequilibrium of the different types of individual axonal sheaths compared to the descriptions of a normal plexus. The possible role of this anomaly in the genesis of intestinal manifestations in this syndrome is here discussed.
D005260:Female; D005729:Ganglioneuroma / Q000473:pathology* / Q000648:ultrastructure; D006801:Humans; D007223:Infant; D007414:Intestinal Neoplasms / Q000473:pathology* / Q000648:ultrastructure; D009377:Multiple Endocrine Neoplasia / Q000473:pathology* / Q000648:ultrastructure; D009197:Myenteric Plexus / Q000473:pathology* / Q000648:ultrastructure
Etude histologique et ultrastructurale d'une ganglioneuromatose intestinale. Syndrome de néoplasie endocrine multiple du type IIb.