title: [Ferrokinetic studies in haemoglobin Wien haemolytic anaemia (author's transl)].
abstract: Ferrokinetic studies in two patients with haemolytic anaemia due to haemoglobin Wien revealed increased haemoglobin synthesis and an increase in effective erythropoiesis. Haemolysis is due to an instability of the haemoglobin itself. The spleen does not appear to play any appreciable role in the aetiology of this condition. There was no extramedullary erythropoiesis in our patients.
mesh_terms: D000293:Adolescent; D000328:Adult; D000743:Anemia, Hemolytic / Q000235:genetics / Q000378:metabolism*; D001728:Dicumarol / Q000627:therapeutic use; D004920:Erythropoiesis; D005260:Female; D006455:Hemoglobins, Abnormal; D006801:Humans; D007501:Iron / Q000378:metabolism*; D008168:Lung / Q000000981:diagnostic imaging; D008297:Male; D011655:Pulmonary Embolism / Q000188:drug therapy; D011877:Radionuclide Imaging; D013154:Spleen / Q000503:physiopathology
chemical_list: D006455:Hemoglobins, Abnormal; D001728:Dicumarol; D007501:Iron
vernacular_title: Eisenkinetische Untersuchungen bei der Hämoglobinopathie Wien.