title: [Pulmonary valve atresia with intact interventricular septum in the grown child and the adult].
abstract: Atresia of the pulmonary valve with an intact interventricular septum is a rare cyanotic congenital cardiac malformation. Rare at birth, it is exceptionally rare for cases to survive over 5 years. Three cases of porlonged survival aged eleven nineteen and thirty-four years are reported. In the latter case, the abnormality was probably aquired. Prolonged survival is related to a collateral pulmonary circulation. Surgical treatment is discussed with respect to the anatomical features. Good results were obtained in the two operated cases.
mesh_terms: D000328:Adult; D002648:Child; D005260:Female; D006346:Heart Septum; D006801:Humans; D008297:Male; D011651:Pulmonary Artery; D011652:Pulmonary Circulation; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery
vernacular_title: L'atrésie valvulaire pulmonaire avec septum interventriculaire intact chez le grand enfant et chez l'adulte.