Malignant schwannoma of the stomach in a patient with von Recklinghausen's disease.
A patient with von Recklinghausen's disease died with a malignant schwannoma of the stomach and was found at autopsy to have neurofibromatosis of the gastrointestinal tract, a plexiform neurofibroma of the myocardium and a phaechromocytoma. Malignancy of the gastrointestinal tract in von Recklinghausen's disease is rare, and this case highlights the difficulties in histological diagnosis of malignant nerve sheath tumours.
D000310:Adrenal Gland Neoplasms / Q000473:pathology; D000368:Aged; D005260:Female; D006338:Heart Neoplasms / Q000473:pathology; D006801:Humans; D007414:Intestinal Neoplasms / Q000473:pathology; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D009442:Neurilemmoma / Q000473:pathology*; D009456:Neurofibromatosis 1 / Q000473:pathology*; D010673:Pheochromocytoma / Q000473:pathology; D013274:Stomach Neoplasms / Q000473:pathology*