title: [Cleido-cranial dysplasia--two observations].
abstract: The radiological changes of cleido-cranial dysplasia are described on the basis of two cases. Special attention is paid to the dental and facio-maxillary aspects. The main features are: (1) Supernumerary teeth, persistence of the first dentition, retention of the second dentition. (2) Open fontanelles and sutures and intercalary bones. (3) Hypo- or aplasia of the clavicles. (4) Defects in the vertebral neural arches and (5) dehiscence of the symphysis due to absent or delayed ossification of the pubis and ischium.
mesh_terms: D000328:Adult; D002648:Child; D002968:Clavicle / Q000002:abnormalities; D002973:Cleidocranial Dysplasia / Q000000981:diagnostic imaging* / Q000235:genetics; D005260:Female; D006801:Humans; D008297:Male; D009999:Ossification, Heterotopic / Q000000981:diagnostic imaging; D010375:Pedigree; D011630:Pubic Bone / Q000000981:diagnostic imaging; D011859:Radiography; D014094:Tooth, Deciduous; D014096:Tooth, Supernumerary / Q000000981:diagnostic imaging
vernacular_title: Die Dysplasia cleidocranialis--Zwei Einzelbeobachtungen.