Von Hippel-Lindau's Disease, syringomyelia and multiple endocrine tumors: a complex neuroendocrinopathy.
A patient presenting with von Hippel-Lindau's disease, syringomyelia, bilateral pheochromocytoma and a multihormonal pancreatic tumor is described. We suggest that this syndrome results from a complex neuroendocrine disorder.
D000236:Adenoma / Q000473:pathology; D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000473:pathology; D000328:Adult; D000798:Angiomatosis / Q000150:complications* / Q000473:pathology; D001344:Autopsy; D006801:Humans; D008297:Male; D010190:Pancreatic Neoplasms / Q000150:complications* / Q000473:pathology; D010673:Pheochromocytoma / Q000150:complications* / Q000473:pathology; D012171:Retinal Vessels; D013577:Syndrome; D013595:Syringomyelia / Q000150:complications* / Q000473:pathology