The radiologic and pathologic spectrum of the prune belly syndrome. The importance of urethral obstruction in prognosis.
The definition, history, and clinical presentation of the prune belly syndrome are outlined. Review of autopsy material and survivors reveal three groups of patients, and the author describes the choices of management available for both groups. Highlighted is the role of the radiologist.
D000009:Abdominal Muscles / Q000002:abnormalities*; D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging; D005145:Face / Q000002:abnormalities; D006801:Humans; D007231:Infant, Newborn; D007668:Kidney / Q000002:abnormalities; D008297:Male; D011379:Prognosis; D013577:Syndrome; D013737:Testis / Q000002:abnormalities*; D014522:Urethral Diseases / Q000150:complications*; D014564:Urogenital Abnormalities; D014567:Urography; D014718:Vesico-Ureteral Reflux / Q000150:complications