title: [Macular changes in pigmentary retinopathy].
abstract: Macular alterations in pigmentary retinopathy may be divised into three groups: 1) Macular lesions in global tapeto retinal degeneration in Leber's disease with a chorioretinal aplasia involving at once both central peripheric retina. 2) Late macular degenerative phenomenons associated to pigmentary retinopathy, and presenting various ophthalmoscopic aspects. --atrophic macular degeneration;--isolated microkystic macular degeneration;--lamellar hote;--microkystic macular degeneration involving vitreous modifications (Goldmann-Favre's disease). 3) Kystoidal macular oedema in pigmentary retinopathy. These different aspects are studied on the ophthalmoscopic, fluorographic, functional, genetic and anatomo-pathologic points of view from our personnal study and a survey of the different observations found in literature. Their ethiopathogenesis remains hypothetic.
mesh_terms: D004487:Edema / Q000473:pathology; D006801:Humans; D007849:Laurence-Moon Syndrome / Q000473:pathology; D008266:Macula Lutea / Q000473:pathology*; D008268:Macular Degeneration / Q000235:genetics / Q000473:pathology; D012162:Retinal Degeneration / Q000473:pathology*; D012174:Retinitis Pigmentosa / Q000235:genetics / Q000473:pathology*; D013577:Syndrome; D014792:Visual Acuity
vernacular_title: Les altérations maculaires de la rétinopathie pigmentaire