Left ventricular outflow obstruction in Taussig-Bing malformation.
In a patient recently undergoing total intracardiac repair of the Taussing-Bing malformation the immediate cause of death appeared to be an obstruction to left ventricular outflow. Examination of this and other specimens of Taussig-Bing malformations revealed that the obstruction appeared to be a portion of the pulmonary conus. This area may be overlooked in the preoperative evaluation and is so located that the obstructive nature of this muscle mass may not be appreciated at the time of surgical repair. The obstructive part of the pulmonary conus can be excised and this appears to be a more common component of the Taussig-Bing anomaly than has previously been appreciated.
D000790:Angiocardiography; D002302:Cardiac Output; D002306:Cardiac Volume; D006332:Cardiomegaly / Q000473:pathology; D002315:Cardiopulmonary Bypass; D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006330:Heart Defects, Congenital / Q000601:surgery*; D006345:Heart Septal Defects, Ventricular / Q000601:surgery*; D006352:Heart Ventricles / Q000473:pathology / Q000503:physiopathology*; D006801:Humans; D007223:Infant; D013577:Syndrome; D014188:Transposition of Great Vessels / Q000601:surgery*