title: [Organic dementia as a first symptom of infantile Huntington's chorea (author's transl)].
abstract: A loss of intellectual capacity at the age of 10 was the first symptom in a case of infantile Huntington's chorea. Subsequently a rigid hypokinetic syndrome occurred only at the age of 20. The dementia syndrome was confirmed in psychological tests. Auxiliary findings such as a diffuse abnornal EEG, as well as a dilatation of the lateral ventricles and an extension of the subarachnoid spaces in the PEG corresponded to a positive diagnosis of Huntington's chorea.
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D003937:Diagnosis, Differential; D003951:Diagnostic Errors; D004569:Electroencephalography; D005260:Female; D006801:Humans; D006816:Huntington Disease / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D001523:Mental Disorders / Q000209:etiology*; D009461:Neurologic Manifestations; D010375:Pedigree
vernacular_title: Organische Demenz als erstes Symptom einer kindlichen Chorea Huntington