[Atresia of the pulmonary artery with intact interventricular septum. Apropos of 2 cases with prolonged course].
The authors report two cases of atresia of the pulmonary outflow with an intact interventricular septum; they are remarkable for their slow progression. In one patient the pulmonary perfusion was furnished by systemic arteries, while in the other it was by way of a patent ductus arteriosus. This second patient died following an attempted bi-cavo-pulmonary anastomosis. Such slow progression, which is the exception, is only possible if there is a substantial vicarious pulmonary circulation.
D000293:Adolescent; D006332:Cardiomegaly / Q000000981:diagnostic imaging; D002648:Child; D004374:Ductus Arteriosus, Patent / Q000601:surgery; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery; D006350:Heart Valve Prosthesis; D006801:Humans; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D011859:Radiography; D014261:Tricuspid Valve / Q000002:abnormalities
Atrésie de l'artère pulmonaire à septum interventriculaire intact. A propos de deux observations d'évolution prolongée