Sézary's syndrome and generalized plane xanthoma.
The first case of Sézary's syndrome associated with generalized plane xanthoma is reported, thereby extending the association of lymphoreticular proliferative disorders with plane xanthomatosis. The association of Sézary's syndrome with plane xanthomatosis may be an in vivo example of defective cell regulation involving the major cellular components of the immune response.
D000328:Adult; D003873:Dermatitis, Exfoliative / Q000150:complications* / Q000473:pathology; D005260:Female; D006801:Humans; D008206:Lymphatic Diseases / Q000150:complications* / Q000473:pathology; D012867:Skin / Q000473:pathology; D013577:Syndrome; D014973:Xanthomatosis / Q000150:complications* / Q000473:pathology