[Renovascular hypertension in neurofibromatosis. Simultaneous occurrence of multiple abdominal and cerebral vascular abnormalities (author's transl)].
Vascular involvement in von Recklinghausen's neurofibromatosis has been known since the work of Reubi (1944, 1946). We found 72 cases of neurofibromatosis with renovascular hypertension reported in the literature. We have observed three female patients, of whom two had unilateral renal artery abnormalities consisting of stensoses and small aneurysms. The third patient, who had a right-sided nephrectomy for probable occlusion of the renal artery, had a coarctation of the abdominal aorta and complete occlusion of the left renal artery and of the coeliac-mesenteric trunk. There were, in addition, large, bilateral aneurysms in the circle of Willis.
D000328:Adult; D000783:Aneurysm / Q000150:complications; D001018:Aortic Diseases / Q000150:complications; D002339:Carotid Arteries; D003097:Collateral Circulation; D005260:Female; D006801:Humans; D006977:Hypertension, Renal / Q000150:complications* / Q000209:etiology; D002532:Intracranial Aneurysm / Q000150:complications; D007738:Kyphosis / Q000150:complications; D009456:Neurofibromatosis 1 / Q000150:complications*; D012077:Renal Artery / Q000002:abnormalities; D012078:Renal Artery Obstruction / Q000150:complications
Renovaskuläre Hypertension bei Neurofibromatose. Gleichzeitig Kasuistik multipler abdominaler und zerebraler Gefässveränderungen