Truncus arteriosus and previous pulmonary arterial banding: clinical and hemodynamic assessment.
Twenty-seven patients with truncus arteriosus and previous pulmonary arterial banding were evaluated 1 1/2 to 14 years (mean 7 years) after banding. Ages at the time of cardiac catheterization ranged from 3 to 18 years (mean 9 years). Current symptoms were severe in five patients and were related to truncal valve incompetence or decreased pulmonary blood flow (or both) rather than to age, duration of palliation or band location. Twenty-one of 22 patients with two pulmonary arteries were considered to be in a hemodynamically operable state at the time of study. The condition of three of five patients with a single pulmonary artery was subsequently found inoperable because of severe pulmonary vascular disease in the lung supplied by the single pulmonary artery. In patients with two pulmonary arteries, demonstration of low pressure in at least one normal-sized pulmonary artery established operability. Postoperative pressure measurements correlated well with preoperative prediction of operability, with 19 of 20 patients having a pulmonary arterial pressure less than 70 percent of systemic levels after repair. Bilateral pulmonary arterial binding may be more effective than central arterial banding (which frequently produces severe obstruction to the right pulmonary artery) in preventing pulmonary vascular obstructive disease in patients with truncus arteriosus who have two pulmonary arteries. Patients with truncus arteriosus and a single pulmonary artery with pulmonary arterial banding remain at high risk for the development of pulmonary vascular obstructive disease.
D000293:Adolescent; D001794:Blood Pressure; D006328:Cardiac Catheterization; D006332:Cardiomegaly / Q000503:physiopathology; D002648:Child; D002675:Child, Preschool; D004562:Electrocardiography; D005080:Exercise Test; D005260:Female; D005500:Follow-Up Studies; D006333:Heart Failure / Q000503:physiopathology; D006439:Hemodynamics; D006801:Humans; D008297:Male; D011183:Postoperative Complications / Q000503:physiopathology*; D011651:Pulmonary Artery / Q000601:surgery*; D011652:Pulmonary Circulation; D014338:Truncus Arteriosus / Q000503:physiopathology; D014339:Truncus Arteriosus, Persistent / Q000503:physiopathology* / Q000601:surgery; D014655:Vascular Resistance