[Essential cryoglobulinemia with accompanying angioneurotic edema].
A case report of a patient with essential cryoglobulinemia and episodes of angioedema caused by an acquired C1 inhibitor deficiency is presented. The patient had high levels of circulating immune complexes. In the course of complement activation C1 inhibitor may be consumed and the resulting C1 inhibitor deficiency led to the occurrence of angioedema.
D000328:Adult; D000799:Angioedema / Q000276:immunology*; D003174:Complement C1 Inactivator Proteins / Q000172:deficiency; D003176:Complement C3 / Q000276:immunology; D003450:Cryoglobulins / Q000032:analysis*; D005260:Female; D006801:Humans; D007105:Immune Complex Diseases / Q000276:immunology; D007074:Immunoglobulin G / Q000276:immunology; D007075:Immunoglobulin M / Q000276:immunology
D003174:Complement C1 Inactivator Proteins; D003176:Complement C3; D003450:Cryoglobulins; D007074:Immunoglobulin G; D007075:Immunoglobulin M
Essentielle Kryoglobulinämie mit passagerem angioneurotischem Odem.