title: Progressive nodular histiocytoma.
abstract: Extensive evaluation of the condition of a 9-year-old girl with a previously undescribed proliferative histocytic syndrome showed normal serum and tissue lipid values, which rule out the known lipid storage diseases. Clinically and histologically the case is inconsistent with any of the recognized xanthomatoses or histiocytic abnormalities.
mesh_terms: D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006099:Granuloma / Q000175:diagnosis / Q000473:pathology; D018219:Histiocytoma, Benign Fibrous / Q000175:diagnosis / Q000378:metabolism / Q000473:pathology; D006801:Humans; D008064:Lipidoses / Q000151:congenital; D008055:Lipids / Q000097:blood; D012878:Skin Neoplasms / Q000175:diagnosis / Q000378:metabolism / Q000473:pathology; D014972:Xanthogranuloma, Juvenile / Q000175:diagnosis / Q000473:pathology; D014973:Xanthomatosis / Q000175:diagnosis / Q000473:pathology
chemical_list: D008055:Lipids