End-to-side anastomosis of the mesenteric vein to the inferior vena cava in the treatment of glycogen storage disease: case report.
A 2-year-old boy with Type I glycogen storage disease received an end-to-side anastomosis of the mesenteric vein to the inferior vena cava with marked improvement in his biochemical factors and nutritional status and with shrinkage of the liver. The efficacy and simplicity of this technique and its lack of complications, as evidenced by follow-up studies over a 4 year period, suggest that its further use is warranted.
D000641:Ammonia / Q000097:blood; D001786:Blood Glucose; D002675:Child, Preschool; D002784:Cholesterol / Q000097:blood; D005952:Glucose-6-Phosphatase / Q000032:analysis; D005953:Glycogen Storage Disease Type I / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008099:Liver / Q000473:pathology; D008297:Male; D008642:Mesenteric Veins / Q000601:surgery*; D011877:Radionuclide Imaging; D014682:Vena Cava, Inferior / Q000601:surgery*
D001786:Blood Glucose; D000641:Ammonia; D002784:Cholesterol; D005952:Glucose-6-Phosphatase