[Primary intestinal lymphangiectasis or Waldmann's disease (author's transl)].
The authors report the observation of a primary intestinal lymphangiectasy diagnosed on a young girl sent for isolated edema of her inferior members, recently appeared. Clinical examination was normal. Biology found a low protein rate at 33 g/l and a low lymph rate : 183 L/mm3. Hepatic and renal records were normal. Test to marked albumin asserted the exsudative enteropathy with a fecal radio-activity of 3.6% (N 1%). Biopsy of the small intestines set out lymphangiectasies of the intestinal mucosa. Referring to this observation and to literature date, the authors realise a clinical and physiopathological analysis of Waldmann's disease or primary intestinal lymphangiectasy.
D000328:Adult; D002648:Child; D002784:Cholesterol / Q000097:blood; D004487:Edema / Q000209:etiology; D005260:Female; D006801:Humans; D007019:Hypoproteinemia / Q000209:etiology; D007421:Intestine, Small / Q000000981:diagnostic imaging / Q000473:pathology; D007866:Leg; D008201:Lymphangiectasis, Intestinal / Q000097:blood / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology; D008220:Lymphography; D008231:Lymphopenia / Q000209:etiology; D008297:Male; D011504:Protein-Losing Enteropathies / Q000209:etiology*
D002784:Cholesterol
Lymphangiectasie intestinale primitive ou maladie de Waldmann.