[Cutis verticis gyrata, hypertrophic gastritis, motrice diarhea, and horse's tall syndrome, a new association an apudoma (carcinoid or chemodectoma) (author's transl)].
The authors report the observation of a 70 years male with Cutis Verticis Gyrata (without hypertrophying osteopathy), Menetrier's hypertrophic gastritis, motrice diarrhea of the endocrine type, flush syndrom, liver angiomatosis and a large sacral water clear cells tumor with horse's tail syndrom. The initial tumor was on the posterior wall of rectum, but was necrosed : bone metastasing chemodectoma, or locally invading carcinoid ? This new complex paraneoplastic disease seems to be associated with APUD tumor.
D000172:Acromegaly / Q000209:etiology; D000368:Aged; D001079:Apudoma / Q000150:complications* / Q000175:diagnosis; D003937:Diagnosis, Differential; D003967:Diarrhea / Q000209:etiology*; D005756:Gastritis / Q000209:etiology*; D006801:Humans; D006984:Hypertrophy; D008297:Male; D010236:Paraganglioma, Extra-Adrenal / Q000150:complications* / Q000175:diagnosis; D012004:Rectal Neoplasms / Q000150:complications* / Q000175:diagnosis; D012447:Sacrum; D012536:Scalp Dermatoses / Q000209:etiology*; D013577:Syndrome
Cutis verticis gyrata, gastrite hypertrophique géante, diarrhée motrice et syndrome de la queue de cheval. Une nouvelle association révélatrice d'un apudome (carcinoïde ou chémodectome?)