[ADAM complex--maxillofacial abnormalities and abnormalities of the extremities caused by amniotic strangulations].
The anomalies of the ADAM complex arise through amniotic strangulations, adhesions and amputations. In the face cleft formations, displacements and deformities of various structures occur. The limbs exhibit constriction grooves, secondary syndactyle or amptuations. According to observations on 8 patients and information from the literature, the presentation of Adam complexes can vary to an extraordinary degree. The anomalies result from exogenous influences. In genetic counselling phenotypically similar congenital malformations must be separated.
D000015:Abnormalities, Multiple / Q000209:etiology*; D002971:Cleft Lip / Q000150:complications; D002972:Cleft Palate / Q000150:complications; D003025:Clubfoot / Q000150:complications; D005260:Female; D005532:Foot Deformities, Congenital; D006228:Hand Deformities, Congenital; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D008445:Maxillofacial Development; D008588:Meningocele / Q000150:complications; D010641:Phenotype; D013576:Syndactyly / Q000150:complications
ADAM-Komplex -- Anomalien des Gesichtsschädels und der Extremitäten infolge amniotischer Abschnürungen.