Von Gierke's disease: report of case.
Von Gierke's disease, or hepatorenal glycogenesis, type I, presents an interesting challenge to the dental practitioner. Showing an incidence of 1/400,000, it is a fairly rare occurrence. It indicates the importance of proper medical consultation in treating these children, and proper dental treatment and preventive programs to alleviate what could be dangerous for these patients.
D000293:Adolescent; D003731:Dental Caries / Q000628:therapy; D003777:Dental Prophylaxis; D003793:Dental Restoration, Permanent; D005884:Gingival Hemorrhage / Q000628:therapy; D005953:Glycogen Storage Disease Type I; D006801:Humans