Gorlin's syndrome and the heart.
Three further cases of the Multiple Basal Cell Naevi Syndrome are added to the literature. One case developed a neonatal left ventricular fibroma, subsequently successfully excised. An association between the syndrome and cardiac tumours has not been documented before, and the relative frequencies of the two conditions are discussed. Biochemical, radiological and chromosomal studies are evaluated and the rate of growth of odontogenic keratocysts discussed.
D000293:Adolescent; D001478:Basal Cell Nevus Syndrome / Q000235:genetics / Q000473:pathology*; D002280:Basal Cell Carcinoma / Q000473:pathology*; D002648:Child; D005260:Female; D005350:Fibroma / Q000473:pathology*; D006338:Heart Neoplasms / Q000473:pathology*; D006801:Humans; D008297:Male; D008439:Maxillary Diseases / Q000473:pathology; D008875:Middle Aged; D009807:Odontogenic Cysts / Q000473:pathology; D010375:Pedigree