Cicatricial pemphigoid with circulating antibasement membrane antibodies. Report of three atypical cases.
3 patients had cicatricial pemphigoid with positive indirect immunofluorescence to basement membrane. 1 patient had remarkably mid disease; another had high titers of autoantibody; and the third was partially responsive to sulfapyridine. All 3 patients were women, as has been true most other reported cases. Antibody titers seemed to correlate with disease activity but not with disease extent.
D000328:Adult; D000368:Aged; D001323:Autoantibodies / Q000032:analysis; D001485:Basement Membrane / Q000276:immunology*; D002921:Cicatrix / Q000276:immunology; D005260:Female; D005455:Fluorescent Antibody Technique; D006801:Humans; D007106:Immune Sera; D008875:Middle Aged; D012872:Skin Diseases, Vesiculobullous / Q000276:immunology*
D001323:Autoantibodies; D007106:Immune Sera