title: [Primary hereditary cristalline corneal dystrophy of Schnyder. Histopathology and ultrastructure (author's transl)].
abstract: The present study consists of light- and electron-microscopic examination of excised cornea in a case of lipid keratopathy (Schnyder) in which a perforating keratoplasty was performed. It demonstrates the deposition of cristalline and non-cristalline substances in the corneal epithelium as well as the anterior half of the corneal stroma. Histiocytic elements infiltrate the subepithelial connective tissue. Bowman's membrane is conspicuously almost totally missing. The paper concludes with a discussion of the above findings.
mesh_terms: D000368:Aged; D003315:Cornea / Q000473:pathology / Q000648:ultrastructure; D003317:Corneal Dystrophies, Hereditary / Q000235:genetics* / Q000473:pathology; D003318:Corneal Opacity / Q000235:genetics* / Q000473:pathology; D004848:Epithelium / Q000648:ultrastructure; D006644:Histiocytes / Q000648:ultrastructure; D006801:Humans; D008297:Male; D013577:Syndrome
vernacular_title: Primäre hereditäre kristalline Hornhautdegeneration (Degeneratio corneae cristallinea hereditaria Schnyder). 1. Mitteilung licht-und elektronenmikroskopischer Befunde.