Type I histiocytosis X presenting as biliary atresia. A case report.
Histiocytosis X may present in a variety of ways. We report a patient who presented with the unusual feature of infiltration of the hepatic duct with histiocytes, manifesting as biliary atresia.
D001660:Biliary Tract Diseases / Q000150:complications; D002779:Cholestasis / Q000209:etiology*; D006500:Hepatic Duct, Common / Q000473:pathology*; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000473:pathology; D006801:Humans; D007223:Infant; D008099:Liver / Q000473:pathology; D008168:Lung / Q000473:pathology; D008297:Male; D012872:Skin Diseases, Vesiculobullous / Q000150:complications