[Idiopathic periostal hyperostosis with dysproteinemia (author's transl)].
The idiopathic periostal hyperostosis with dysproteinemia shows typical symptoms: acute onset with high fever and severe pain in the forearms and the praetibial area, periostal reaction along the ulnae and tibiae accompanied by hypalbuminemia and alpha2-globulin increase. The clinical entity has yet been described in only 2 cases. Our own case illustrates the longterm follow-up. The differential diagnosis especially of Caffey-Syndrom is discussed.
D001848:Bone Diseases, Developmental / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging; D002648:Child; D003937:Diagnosis, Differential; D006801:Humans; D006958:Hyperostosis, Cortical, Congenital / Q000175:diagnosis; D007070:Immunoglobulin A / Q000032:analysis; D007074:Immunoglobulin G / Q000032:analysis; D007075:Immunoglobulin M / Q000032:analysis; D008297:Male; D010265:Paraproteinemias / Q000097:blood / Q000150:complications*; D010521:Periosteum / Q000000981:diagnostic imaging; D011859:Radiography; D012709:Serum Albumin / Q000032:analysis; D012712:Serum Globulins / Q000032:analysis; D013577:Syndrome; D014457:Ulna / Q000000981:diagnostic imaging
D007070:Immunoglobulin A; D007074:Immunoglobulin G; D007075:Immunoglobulin M; D012709:Serum Albumin; D012712:Serum Globulins
Die idiopatische periostale Hyperostose mit Dysproteinämie.