Epidermolysis bullosa: current concepts and management of the advanced hand deformity.
A current classification of the types of epidermolysis bullosa is reviewed, in conjunction with some etiological concepts. The pathomechanics of the advanced hand deformity are discussed, and applied to a sequential plan of reconstructive surgery. The objective is the restoration of elementary hand function. Two illustrative cases are presented.
D000293:Adolescent; D000328:Adult; D003286:Contracture / Q000209:etiology / Q000601:surgery; D004820:Epidermolysis Bullosa / Q000150:complications / Q000601:surgery* / Q000628:therapy; D005260:Female; D006227:Hand Deformities, Acquired / Q000209:etiology / Q000601:surgery* / Q000628:therapy; D006801:Humans; D008297:Male; D016038:Skin Transplantation; D014182:Transplantation, Autologous