Surgical correction of the hand in epidermolysis bullosa dystrophica.
Epidermolysis bullosa dystrophica (polydysplastic type) is a rare congenital skin anomaly which, in the hands, because they are exposed to repeated trauma, results in a severe "mitten"-like deformity. Functional benefit was obtained in three patients by separation of the digits and application of split-thickness grafts. Wolfe grafts or "split-off" (epidermis) grafts. Arthrodesis of the interphalangeal joints and filleting of the little finger to provide a flap which could be turned in to the palm, resulted in an improvement in hand function.
D000293:Adolescent; D000328:Adult; D002294:Carcinoma, Squamous Cell / Q000150:complications / Q000601:surgery; D004820:Epidermolysis Bullosa / Q000150:complications / Q000601:surgery*; D005260:Female; D005385:Fingers / Q000601:surgery*; D006227:Hand Deformities, Acquired / Q000601:surgery*; D006801:Humans; D012878:Skin Neoplasms / Q000150:complications / Q000601:surgery; D016038:Skin Transplantation; D014182:Transplantation, Autologous