Juvenile fibromatosis and other diseases of connective tissue.
There are a number of features which are common to such variable conditions as juvenile fibromatosis on the one hand and torticollis and congenital dislocation of the hip, and possibly scoliosis, on the other. Various pathological syndromes are presented, all of them characterized by disturbance and contracture of connective tissue. Surgery is carried out in severe cases when it is a practicable proposition. The administration of an enzyme inhibitor at cellular level has introduced a new dimension in the management of localized fibromatosis.
D001720:Birth Injuries / Q000150:complications; D003025:Clubfoot / Q000628:therapy; D003240:Connective Tissue Diseases / Q000473:pathology*; D005350:Fibroma / Q000473:pathology*; D006618:Hip Dislocation, Congenital / Q000209:etiology / Q000628:therapy; D006801:Humans; D007223:Infant; D008297:Male; D012600:Scoliosis / Q000209:etiology; D014103:Torticollis / Q000151:congenital / Q000473:pathology