Sprengel's deformity. Radiology of the pathologic deformation.
A unique specimen of unilateral Sprengel's deformity, and contralateral normal pectoral girdle, were studied morphologically and roentgenographically. The cervical spine exhibited multiple abnormalities involving both the vertebral centra as well as the posterior elements (Klippel-Feil abnormality). A small spina bifida involving C5 and C6 was present. Abnormalities of the spinous processes included an articulation with a well-formed omovertebral bone that also articulated with the vertebral (infraspinatus) margin of the scapula. Secondary (presumed epiphyseal) ossification was present in the omovertebral bone at the distal end. The scapula was deformed, especially in the supraspinatus portion. The clavicle was shorter and had a different contour.
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging; D000293:Adolescent; D006801:Humans; D007714:Klippel-Feil Syndrome / Q000000981:diagnostic imaging; D008297:Male; D011859:Radiography; D012540:Scapula / Q000002:abnormalities*; D012600:Scoliosis / Q000000981:diagnostic imaging*; D016136:Spina Bifida Occulta / Q000000981:diagnostic imaging; D013577:Syndrome