Hearing patterns in Morquio's syndrome (mucopolysaccharidosis IV).
The hearing status of 18 patients with Morquio's syndrome (mucopolysaccharidosis IV) was evaluated. All three patients under age 8 years had a conductive hearing loss. Fourteen of 15 patients 8 years of age and older had a mixed or sensorineural hearing loss; one had normal hearing. Six patients wore hearing aids. By the end of the first decade of life, most persons with Morquio's syndrome may be expected to have either a mixed or sensorineural hearing loss. Amplification may be required.
D000293:Adolescent; D000328:Adult; D001844:Bone Conduction; D002648:Child; D002675:Child, Preschool; D005260:Female; D006309:Hearing; D006311:Hearing Disorders / Q000150:complications*; D006801:Humans; D008297:Male; D009085:Mucopolysaccharidosis IV / Q000150:complications* / Q000503:physiopathology; D010033:Otitis Media / Q000150:complications; D012008:Recurrence