[Multiple vascular stenoses in neurofibromatosis (author's transl)].
Vascular lesions due to neurofibromatosis have been predominantly reported in the renal arteries as cause of arterial hypertension, but they can occur everywhere. The angiography shows a smoothly bordered stenosis at the origin of the artery with an elongated funnel shaped poststenotic deformity. Collateral vessels are often present. Reconstructive arterial surgery is in a high percentage successful. The main differential diagnosis includes fibromuscular dysplasia. Arterial hypertension in a young person with neurofibromatosis should suggest the presence of pheochromocytoma or renovascular disease.
D001157:Arterial Occlusive Diseases / Q000150:complications / Q000209:etiology*; D002339:Carotid Arteries; D002648:Child; D003097:Collateral Circulation; D003937:Diagnosis, Differential; D006801:Humans; D006973:Hypertension / Q000209:etiology; D007668:Kidney / Q000098:blood supply; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D012078:Renal Artery Obstruction / Q000209:etiology; D014652:Vascular Diseases / Q000175:diagnosis
Multiple Gefässstenosen bei Neurofibromatose von Recklinghausen