Congenital retroperitoneal hemangioendothelioma with Kasabach-Merritt syndrome.
This is the first documented congenital retroperitoneal hemangioendothelioma. The patient presented at birth with a retroperitoneal mass and thrombocytopenia. Postmortem examination revealed the tumor to be a hemangioendothelioma, arising from the posterior abdominal wall. The association of an angiomatous tumor will thrombocytopenia represents the Kasabach-Merritt syndrome.
D006390:Hemangioendothelioma / Q000150:complications / Q000151:congenital*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012186:Retroperitoneal Neoplasms / Q000150:complications / Q000151:congenital*; D013577:Syndrome; D013921:Thrombocytopenia / Q000150:complications*