[Benign chronic conjugated hyperbilirubinaemia: rotor syndrome or hepatic storage impairment?].
In a 52-year-old female who was jaundiced since early childhood, marked conjugated hyperbilirubinaemia and a delay of bromsulfophthalein and indocyanine green plasma disappearance rates were observed. Liver histology, plasma bile acids and plasma clearance of 14-C-cholic acid were normal. There was a pronounced impairment of the relative storage capacity of bromsulfophthalein (S = 2,4 mg/mg%) and a moderate decrease of BSP-transport maximum.
D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D006933:Hyperbilirubinemia, Hereditary / Q000175:diagnosis*; D007566:Jaundice, Chronic Idiopathic / Q000175:diagnosis; D008099:Liver / Q000473:pathology; D008111:Liver Function Tests; D008875:Middle Aged; D013448:Sulfobromophthalein; D013577:Syndrome
D013448:Sulfobromophthalein
Benigne chronische konjugierte Hyperbilirubinämie: Rotor-Syndrom oder hepatischer Speicherdefekt?