Congenital intrathoracic bronchopulmonary foregut malformations in childhood.
Bronchopulmonary foregut malformations (BPFM) are a group of related disorders. They include tracheoesophageal fistula with or without atresia, bronchopulmonary sequestration, intestinal duplication cyst, bronchogenic cyst, aberrant systemic arterial supply to the lung, and bronchial mucosal rests in the esophagus. This paper describes 12 cases which illustrate the spectrum of clinical and radiographic features of these anomalies. The embryogenesis of these malformations is reviewed and appropriate radiographic investigation is discussed.
D001980:Bronchi / Q000002:abnormalities* / Q000196:embryology; D001995:Bronchography; D001998:Bronchopulmonary Sequestration / Q000000981:diagnostic imaging* / Q000196:embryology; D002648:Child; D002675:Child, Preschool; D004947:Esophagus / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000196:embryology; D005260:Female; D006801:Humans; D007223:Infant; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000196:embryology; D008297:Male; D011656:Pulmonary Emphysema / Q000000981:diagnostic imaging