title: Primary rhabdomyosarcoma of the tentorium with peculiar angiographic findings.
abstract: Primary intracranial rhabdomyosarcoma is extremely rare, only nine cases have been reported in the world literature. To differentiate it from medullomyoblastoma, rhabdomyosarcoma should be devoid of neuroblastic elements. A case of rhabdomyosarcoma of the tentorial region in a 17-year-old boy is reported. Carotid angiograms demonstrated a peculiar neovascularity. Multiple cytologic preparations of CSF repeatedly contained rhabdomyosarcoma cells and CSF dissemination in the spinal subarachnoid space was documented at autopsy. The literature is reviewed.
mesh_terms: D000293:Adolescent; D000328:Adult; D000792:Angiography; D001932:Brain Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000628:therapy; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008297:Male; D008527:Medulloblastoma / Q000000981:diagnostic imaging; D008578:Meninges / Q000000981:diagnostic imaging* / Q000473:pathology; D008875:Middle Aged; D011655:Pulmonary Embolism / Q000150:complications; D012208:Rhabdomyosarcoma / Q000000981:diagnostic imaging* / Q000473:pathology / Q000628:therapy