Idiopathic calcific pancreatitis, CRST syndrome and progressive systemic sclerosis.
A 43-year old man with CRST syndrome (calcinosis, Raynaud's phenomenon, sclerodactyly and telangiectasia) and progressive systemic sclerosis presented with a four-year history of relapsing abdominal pain, the result of chronic pancreatitis, not associated with alcoholism, biliary disease, or any of the known causes of pancreatitis. He had a good response to retrograde pancreatic duct drainage but exhibited management problems and complications that may be peculiar to the systemic sclerosis patient with pancreatitis. A cause and effect relationship between progressive systemic sclerosis and pancreatic disease is not proven but we believe there is evidence to suggest such a relationship.
D000328:Adult; D002114:Calcinosis / Q000150:complications*; D002908:Chronic Disease; D005385:Fingers; D006801:Humans; D008297:Male; D010195:Pancreatitis / Q000150:complications*; D011928:Raynaud Disease / Q000150:complications*; D012595:Scleroderma, Systemic / Q000150:complications*; D013577:Syndrome; D013684:Telangiectasis / Q000150:complications*