Successful management of popliteal arterial disruption in Ehlers-Danlos syndrome.
A review of the literature on Ehlers-Danlos syndrome with particular attention to vascular complications enabled us to outline an orderly diagnostic and therapeutic plan which has allowed salvage of an individual with a popliteal false aneurysm. In patients with Ehlers-Danlos syndrome and brachial, superficial femoral, or popliteal arterial disruption, the use of proximal tourniquet control to allow ligation of the disrupted artery under a no-flow, no-pressure situation is recommended. The ligations should be carried out with a large ligature or possibly with large hemoclips and/or reinforced with multiple fine atraumatic vascular sutures distally. These patients may be treated successfully for flexion contractures because of the laxness of their tissues.
D000293:Adolescent; D000783:Aneurysm / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D001157:Arterial Occlusive Diseases / Q000150:complications; D001794:Blood Pressure; D002648:Child; D002675:Child, Preschool; D003025:Clubfoot / Q000150:complications; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis; D005260:Female; D005263:Femoral Artery; D006552:Hernia, Inguinal / Q000150:complications; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011150:Popliteal Artery / Q000601:surgery*; D011247:Pregnancy; D011859:Radiography; D014652:Vascular Diseases / Q000150:complications