[Unilateral dysplasia of the circle of Willis with multiple distal stenoses (author's transl)].
Neurological and clinical examinations were found to be normal in a woman aged 40 years who had had a single generalized epileptic seizure. Rediological examinations demonstrated a spiral-shaped calcification above and laterally to the left sella turcica. This corresponded to changes in the C 1 segment of the left carotid sinus, which was partly stenosed distally, with left unilateral abnormalities of the circle of Willis and multiple distal stenoses of the left sylvian and vertebro-basilar arteries. Scanning demonstrated that these had been present for a long time, but it is not possible to establish the diagnosis on an etiological basis as no similar radiological findings have been published.
D000328:Adult; D001157:Arterial Occlusive Diseases / Q000000981:diagnostic imaging; D002114:Calcinosis / Q000150:complications* / Q000000981:diagnostic imaging; D002340:Carotid Artery Diseases / Q000150:complications* / Q000000981:diagnostic imaging; D002346:Carotid Sinus / Q000000981:diagnostic imaging; D002533:Cerebral Angiography; D002941:Circle of Willis / Q000002:abnormalities* / Q000000981:diagnostic imaging; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D009072:Moyamoya Disease / Q000175:diagnosis
Dysplasie unilatérale du polygone de Willis, associée à des sténoses distales multiples.