Hemispherectomy for Sturge-Weber syndrome.
Patients with Sturge-Weber disease who have the onset of seizures in infancy invariably face a progressively downhill course which leaves them severely hemiplegic, demented and usually institutionalized because of uncontrolled seizures. During the past 12 years, we have carried out 6 hemispherectomies in infants under 1 year of age who presented with seizures and Sturge-Weber disease. The results have been gratifying. Seizures have stopped, hemipareses have been minimal and intellectual development has been good.
D000798:Angiomatosis / Q000601:surgery*; D002114:Calcinosis / Q000000981:diagnostic imaging; D002533:Cerebral Angiography; D002536:Cerebral Arteries / Q000473:pathology; D002540:Cerebral Cortex / Q000473:pathology / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D004569:Electroencephalography; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology; D002534:Hypoxia, Brain / Q000473:pathology; D007223:Infant; D011183:Postoperative Complications / Q000209:etiology; D012640:Seizures / Q000601:surgery; D013341:Sturge-Weber Syndrome / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D013346:Subarachnoid Space; D014057:Tomography, X-Ray Computed