Congenital lipoid nephrosis with left renal vein thrombosis and Chiari's syndrome.
An infant with primary congenital lipoid nephrosis then developed left renal vein thrombosis and secondary hepatic vein obstruction. This was shown by inferior venacavography. The thrombus detached subsequently, and the child died from massive pulmonary embolism.
D001777:Blood Coagulation; D006502:Budd-Chiari Syndrome / Q000000981:diagnostic imaging / Q000209:etiology*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007672:Kidney Cortex / Q000473:pathology; D009402:Nephrosis, Lipoid / Q000150:complications / Q000151:congenital* / Q000000981:diagnostic imaging; D011507:Proteinuria / Q000209:etiology; D011859:Radiography; D012082:Renal Veins / Q000000981:diagnostic imaging; D013927:Thrombosis / Q000000981:diagnostic imaging / Q000209:etiology*