[Xanthoma disseminatum (Montgomery's syndrome) (author's transl)].
Montgomery's syndrome is distinguished by skin and mucous membrane xanthomatosis, predominant on folds, associated with diabetes insipidus and normal lipidic balance. From one typical case history occurring in a young gravida, the authors stresse upon: --Review of literature's cases. --Peculiar therapeutic problems during pregnancy. --Nosological discussion: the position of Montgomery's syndrome compared with histocytosis X and other nonnormolipidic xanthomatosis. This problem is all the more important as in this observation xanthomatosis was first with a normal lipidic measurement, lipidic disorders appearing only secondarily.
D000328:Adult; D003919:Diabetes Insipidus / Q000150:complications; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D050356:Lipid Metabolism; D009092:Mucous Membrane / Q000473:pathology; D011247:Pregnancy; D014973:Xanthomatosis / Q000150:complications / Q000209:etiology / Q000473:pathology* / Q000628:therapy
Xanthoma disseminatum (syndrome de Montgomery).