Early neurosurgical repair in craniofacial dysmorphism.
The authors describe the operative repair and results in 16 cases of craniofacial dysmorphism. The craniofacial dysmorphic states are presumably caused by premature closure of basal skull sutures in combination with the coronal sutures. Hydrocephalus is commonly associated with these conditions and contributes to the bizarre appearance as well as the abnormal mentation that some of these patients display. Early neurosurgical intervention using the procedure of lateral supraorbital ridge advancement yields excellent results in the majority of these infants.
D000015:Abnormalities, Multiple; D000367:Age Factors; D003398:Craniosynostoses / Q000150:complications / Q000235:genetics / Q000601:surgery*; D003399:Craniotomy; D005147:Facial Bones / Q000002:abnormalities*; D005260:Female; D005799:Genes, Dominant; D005808:Genes, Recessive; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008722:Methods; D012886:Skull / Q000002:abnormalities*