Progressive hemifacial atrophy (Parry-Romberg syndrome): report of two cases.
We describe 2 cases of progressive hemifacial atrophy (Parry-Romberg syndrome) with typical facial and ocular involvement. Ocular manifestations in these 2 cases include enophthalmos, due to fat atrophy, decreased corneal sensitivity, episcleritis, and band keratopathy. The slowly progressive changes were documented in one case over a 40 year period. Both cases were unilateral with limitation of the lesions at the midline.
D000273:Adipose Tissue / Q000473:pathology; D000328:Adult; D001284:Atrophy; D003316:Corneal Diseases / Q000175:diagnosis; D005128:Eye Diseases / Q000175:diagnosis*; D005150:Facial Hemiatrophy / Q000175:diagnosis*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D009915:Orbit / Q000473:pathology; D013577:Syndrome; D013997:Time Factors