Multiple simultaneous paragangliomas of the head and neck in association with multiple retroperitoneal pheochromocytomas.
A patient in whom multiple, familial, catecholamine-secreting head and neck paragangliomas and retroperitoneal pheochromocytomas were identified is reported. There were at least nine primary and possibly five recurrent neoplasms, the most reported in a single patient. In patients with family history of pheochromocytoma or paraganglioma or with multiple tumors, careful laboratory and angiographic studies are indicated to discover additional lesions.
D000328:Adult; D005260:Female; D006258:Head and Neck Neoplasms / Q000601:surgery*; D006801:Humans; D009378:Neoplasms, Multiple Primary / Q000601:surgery*; D010235:Paraganglioma / Q000601:surgery*; D010673:Pheochromocytoma / Q000601:surgery*; D012008:Recurrence; D012186:Retroperitoneal Neoplasms / Q000601:surgery*