[Diagnostic value of hemodynamic and angiographic studies in right medioventricular subinfundibulaire stenosis (author's transl)].
Two cases are reported of right medioventricular subinfundibular stenosis with intact intraventricular septum. This rare congenital malformation, also known as "double chambered right ventricle", and usually associated with an intraventricular communication, can only be diagnosed with certainly on the results of hemodynamic and angiographic studies which demonstrate the abnormal medioventricular muscle bands. A steep intraventricular pressure gradient was noted in the first patient who was operated upon successfully. The second patient developed progressively increasing stenosis which underlines the need for long-term observation of cases in which there is little initial obstruction. Particular types of electrocardiographic recordings, not previously reported, were present in both cases; in one there was an unexplained long QT interval; in the other a first degree nodal atrioventricular block with atrial arrhythmia, requiring the implantation of a cardiac stimulator.
D000328:Adult; D000792:Angiography; D002932:Cineangiography; D004562:Electrocardiography; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000503:physiopathology; D006352:Heart Ventricles / Q000002:abnormalities*; D006439:Hemodynamics; D006801:Humans
Les sténoses médioventriculaires droites sous-infundibulaires : un diagnostic hémodynamique et angiographique.