[Massive orbital osteolysis by a chordoma. Report of a case and review of the litterature (author's transl)].
Clinical, radiological and anatomical description of sellar chordoma giving, on a sixty seven years old man, an unusually large tumoral exophthalmos, a massive orbito-sphenoidal osteolysis and a chiasmatic syndroma. Discussion stresses the topographic data of chordoma in connection with the embryonal chordal cell rests. Patterns of evolution and neuro-ophthalmologic symptoms of cephalic chordoma are studied with the literature facts. Morphologic criteria, specifical ones and those differential diagnosis, are exactly scheduled.
D000368:Aged; D001847:Bone Diseases / Q000209:etiology; D001862:Bone Resorption / Q000209:etiology*; D002817:Chordoma / Q000150:complications* / Q000196:embryology / Q000473:pathology; D005094:Exophthalmos / Q000209:etiology; D006801:Humans; D008297:Male; D009915:Orbit / Q000000981:diagnostic imaging; D009918:Orbital Neoplasms / Q000150:complications* / Q000196:embryology / Q000473:pathology; D010014:Osteolysis / Q000209:etiology*; D011859:Radiography; D013100:Sphenoid Bone / Q000000981:diagnostic imaging
Envahissement ostéolytique massif de l'orbite par un chordome. Discussion d'une observation privilégiée et revue de la littérature.