Surgical management of urogenital sinus abnormalities.
This report describes 12 cases of urogenital sinus malformations and their management in female infants, 10 with imperforate anus. Excluded were cases of urogenital sinus malformation secondary to the adrenogenital syndrome or primary sexual ambiguity. Immediate definition of the anatomy by appropritae endoscopy and radiography is essential to plan the correct operative approach. This can be a relatively simple flap vaginoplasty from below, together with perineal anoplasty in some cases. Others may require an extensive combined abdominal-perineal approach with vaginal pullthrough, ureteral reimplantation, creation of a urethra from the urogenital sinus, resection of vaginal septum, and creation of perineal skin flaps to join to the pulled through vagina which may be too short to reach the perineum.
D000293:Adolescent; D001006:Anus, Imperforate / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D014521:Urethra / Q000002:abnormalities / Q000601:surgery; D001743:Urinary Bladder / Q000002:abnormalities; D014564:Urogenital Abnormalities; D014566:Urogenital System / Q000601:surgery*; D014621:Vagina / Q000002:abnormalities / Q000601:surgery