title: [Uncombable hair syndrome].
abstract: Two cases of new hair defect syndrome, recently described by French dermatologists, are reported. They are characterized by clinically dry, bright and uncombable hair. Pathologic and scanning electron microscope studies, show: -- Angulation of the hair bulb with adherence between the inner root sheath and the hair shaft. -- Canalicular formations longitudinally disposed on the cuticular surface with irregular stratification of the external sheath. A malformation of the hair bulb of unknown aetiology is postulated. This malformation, probably familial, is not associated with any other abnormalities. This defect would result in hair shaft surface abnormality.
mesh_terms: D002648:Child; D005260:Female; D006197:Hair / Q000002:abnormalities* / Q000648:ultrastructure; D006801:Humans; D007223:Infant; D012871:Skin Diseases / Q000235:genetics / Q000473:pathology; D013577:Syndrome
vernacular_title: Síndrome de los cabellos "impeinables".