Inner ear malformations with oto-liquorrhea. Tomographic findings in three cases with a mixed hearing impairment.
The paper deals with three boys suffering from a mixed hearing loss. They were all referred to tomography of the temporal bones in order to find some middle ear malformation amenable to surgery. The tomograms revealed identical malformations of the inner ear; the lumen of the labyrinth are found irregularly dilated and the internal acoustic meatus is widened. Its course in the lateral end is abnormal with a downwards turn towards the basal coil of the cochlea. Explorative tympanotomy in one of the patients revealed a severe otoliquorrhea during an attempt to perform a stapedectomy, and this may serve as a warning against operation in patients presenting the mentioned tomographic changes which, once seen, are easily recognized.
D000293:Adolescent; D001299:Audiometry; D002558:Cerebrospinal Fluid Otorrhea / Q000000981:diagnostic imaging / Q000209:etiology*; D002648:Child; D000013:Congenital Abnormalities / Q000150:complications; D007758:Ear, Inner / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006311:Hearing Disorders / Q000000981:diagnostic imaging / Q000209:etiology*; D006801:Humans; D008297:Male; D014056:Tomography, X-Ray