title: [Psychosocial intellectual development of children with infantile cystinosis and cerebral atrophy (author's transl)].
abstract: The psychosocial and intellectual development of 4 boys with nephropathic cystinosis and brain atrophy documented by cranial computerized tomography was investigated by use of biographical data and psychological tests (HAWIK, Deutscher Rechtschreibtest). Inspite of the brain atrophy the patients showed low-normal intellectual capacities and mainly average school performance. There were no psychosocial abnormalities correlated to the primary metabolic disease. However, renal dwarfism led to mascotism requiring psychotherapy.
mesh_terms: D001284:Atrophy; D001921:Brain / Q000473:pathology*; D002648:Child; D002653:Child Behavior Disorders / Q000150:complications; D002657:Child Development; D003554:Cystinosis / Q000523:psychology*; D006801:Humans; D008297:Male; D014888:Wechsler Scales
vernacular_title: Psychosozial-intellektuelle Entwicklung bei Kindern mit infantiler Zystinose und Hirnatrophie.