Biotin activation of carboxylase activity in cultured fibroblasts from a child with a combined carboxylase defect.
D001710:Biotin / Q000494:pharmacology*; D002245:Carbon Dioxide; D002262:Carboxy-Lyases / Q000172:deficiency / Q000378:metabolism*; D002478:Cells, Cultured; D002648:Child; D003437:Crotonates; D004789:Enzyme Activation / Q000187:drug effects; D005347:Fibroblasts / Q000201:enzymology; D006801:Humans; D007700:Kinetics; D008025:Ligases / Q000172:deficiency / Q000378:metabolism*; D011422:Propionates
D003437:Crotonates; D011422:Propionates; D002245:Carbon Dioxide; D001710:Biotin; D002262:Carboxy-Lyases; D008025:Ligases