[Long-time observation of a case of retroperitoneal fibrosis with Klinefelter's syndrome (author's transl)].
The etiology of retroperitoneal fibrosis still is largely unknown. Autoimmunologic mechanisms, traumata, systemic diseases, and drugs have been discussed as possible etiologic factors. The presented case was found to have a Klinefelter's syndrome besides retroperitoneal fibrosis. We do not believe that there is a relation between the two diseases. The retroperitoneal fibrosis of this case responded well to glucocorticosteroid therapy and the severly reduced renal function became normal.
D006801:Humans; D007713:Klinefelter Syndrome / Q000175:diagnosis* / Q000000981:diagnostic imaging; D008297:Male; D008775:Methylprednisolone / Q000627:therapeutic use; D008875:Middle Aged; D011859:Radiography; D012185:Retroperitoneal Fibrosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000188:drug therapy
D008775:Methylprednisolone
Langzeitverlauf bei einem Fall von retroperitonealer Fibrose (M. Ormond) mit Klinefelter-Syndrom.