In vivo and in vitro response of human branched chain alpha-ketoacid dehydrogenase to thiamine and thiamine pyrophosphate.
D005347:Fibroblasts / Q000201:enzymology / Q000648:ultrastructure; D006358:Hot Temperature; D006801:Humans; D066298:In Vitro Techniques; D007651:Keto Acids / Q000652:urine; D007658:Ketone Oxidoreductases / Q000378:metabolism*; D007962:Leukocytes / Q000201:enzymology; D008297:Male; D008375:Maple Syrup Urine Disease / Q000201:enzymology; D008928:Mitochondria / Q000201:enzymology; D013831:Thiamine / Q000494:pharmacology*; D013835:Thiamine Pyrophosphate / Q000494:pharmacology*; D014631:Valerates / Q000378:metabolism
D007651:Keto Acids; D014631:Valerates; D007658:Ketone Oxidoreductases; D013835:Thiamine Pyrophosphate; D013831:Thiamine