Electrophysiological responses in hydranencephaly.
We recorded electrophysiological responses, both electroretinograms (ERGs) and visual evoked responses (VER), at 4 and 21 months of age in a child with hydranencephaly. As expected, the ERG was normal. Despite the apparent absence of most of the cerebral cortex, a VER was present at both visits. The child's visual performance definitely improved both subjectively and electrophysiologically. The VER contained multiple early components in contrast to previous reports, where only a slow, monophasic response was detected.
D000757:Anencephaly / Q000503:physiopathology*; D002675:Child, Preschool; D004596:Electroretinography; D005071:Evoked Potentials; D005260:Female; D006801:Humans; D006832:Hydranencephaly / Q000175:diagnosis / Q000503:physiopathology*; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D014172:Transillumination; D014785:Vision, Ocular; D014793:Visual Cortex / Q000503:physiopathology*