title: [Right aortic arch associated with congenital heart defects].
abstract: The author's experience in the association of right aortic arch and congenital cardiac malformations is reported. We found 56 cases out of 1200 congenital cardiac malformations which constitutes 4.6%. In the classification of Knight and Edwards, type I right aortic arch was the most frequent (96%) and it was associated principally with Tetralogy of Fallot (46%), transposition of the great vessels (14.3%), truncus arteriosus (12%), tricuspid atresia (10.7%) and complex cardiac malformations associated with the syndrome of visceral heterotaxy (10.7%). In type II and type III we found only one case of each and these were associated with pulmonary valvular stenosis, atrial septal defect and ventricular septal defect. It is noted that the right aortic arch has never been associated with total anomalous pulmonary venous return nor with mitral or aortic valvular malformations.
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000196:embryology; D006330:Heart Defects, Congenital / Q000145:classification / Q000150:complications* / Q000196:embryology; D006801:Humans; D007231:Infant, Newborn
vernacular_title: Arco aórtico derecho asociado a cardiopatías congénitas.