Epicardial nodules: a possible sign of coronary endarteritis with hypoplastic right heart syndrome.
Hypoplastic heart syndromes in infancy have been associated with an unusual obliterative coronary endarteritis. Only one case was revealed amont the 16 autopsies performed over the past ten years at The Johns Hopkins Hospital on infants with the hypoplastic right heart syndrome. Grossly visible epicardial nodules at the time of autopsy prompted further investigation in this case and should be considered markers of this unusual entity.
D003327:Coronary Disease / Q000175:diagnosis / Q000473:pathology*; D004692:Endarteritis / Q000175:diagnosis / Q000473:pathology*; D006330:Heart Defects, Congenital / Q000150:complications / Q000473:pathology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010496:Pericardium / Q000473:pathology*