Cardiac conduction abnormalities and Stokes-Adams attacks in myotonic dystrophy.
Myotonic dystrophy is a well known cause of cardiomyopathy. While various cardiac conduction abnormalities have been described in patients with myotonic dystrophy, so far only sporadic cases of Stokes-Adams attacks have been reported. Of 27 patients with this disease various conduction disturbances were detected in 17 (63%), 5 of whom presented with Stokes-Adams attacks and were found to have intracardiac conduction defects. The prognosis in four of the five patients was greatly improved with permanent pacemaker implantation.
D000219:Adams-Stokes Syndrome / Q000209:etiology* / Q000628:therapy; D000328:Adult; D002037:Bundle-Branch Block / Q000209:etiology / Q000628:therapy; D005260:Female; D005500:Follow-Up Studies; D006327:Heart Block / Q000209:etiology* / Q000628:therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D009136:Muscular Dystrophies / Q000150:complications*; D010138:Pacemaker, Artificial