Eosinophilic fasciitis.
Shulman's syndrome includes fasciitis of rapid onset, sclerodermoid skin changes, absence of Raynaud's phenomenon, absence of visceral manifestations of progressive systemic sclerosis, hypergammaglobulinemia, transient eosinophilia, and a dramatic response to systemic corticosteroid therapy. Although this syndrome may be a variant of scleroderma, its dramatic responsiveness to corticosteroid therapy is a particularly distinguishing feature.
D000293:Adolescent; D000328:Adult; D000368:Aged; D003937:Diagnosis, Differential; D004802:Eosinophilia / Q000150:complications* / Q000188:drug therapy; D005205:Fascia / Q000473:pathology; D005260:Female; D006801:Humans; D006942:Hypergammaglobulinemia / Q000150:complications*; D007249:Inflammation / Q000150:complications / Q000188:drug therapy; D008297:Male; D008875:Middle Aged; D011241:Prednisone / Q000627:therapeutic use; D012595:Scleroderma, Systemic / Q000175:diagnosis; D012877:Skin Manifestations; D013577:Syndrome
D011241:Prednisone