Multiple congenital hemangiopericytomas of the head and neck.
Hemangiopericytoma is a vascular tumor arising from contractile cells, the pericyte of Zimmermann. The neoplasms most frequently involve deep musculature; however, 16% occur in the head and neck region. The case presented here represents the rare occurrence of multiple congenital hemangiopericytoma of the head and neck. In older patients, these rather poorly differentiated tumors recur locally after excision in 50%-80% of cases depending on the organ site involved. Distant metastasis to lung or bone may follow. Congenital hemangiopericytomas appear to follow a more benign clinical course, possibly due to a more superficial location and a tendency to transform into hemangioendotheliomas. Recommended treatment is wide local excision and long-term follow-up.
D006258:Head and Neck Neoplasms / Q000151:congenital / Q000601:surgery; D006393:Hemangiopericytoma / Q000151:congenital* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009303:Nasopharyngeal Neoplasms / Q000151:congenital* / Q000601:surgery; D009378:Neoplasms, Multiple Primary / Q000151:congenital* / Q000601:surgery