Pigmented paravenous retinochoroidal atrophy.
A patient with paravenous pigmented chorioretinal atrophy is presented. A differential diagnosis and review of the literature are discussed. Fluorescein angiography confirms the presence of a widespread paravenous retinal pigment epithelial defect with minimally affected choroidal vasculature. The visual fields are constricted in proportion to the extent of the pigmentary abnormality. The electro-oculogram and electroretinogram show reduced responses indicative of a more extensive abnormality than is visible ophthalmoscopically. The etiology and natural course of this entity are unknown.
D000293:Adolescent; D001284:Atrophy; D002829:Choroid / Q000473:pathology*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D010857:Pigment Epithelium of Eye / Q000473:pathology; D010859:Pigmentation Disorders / Q000175:diagnosis / Q000473:pathology*; D012164:Retinal Diseases / Q000175:diagnosis / Q000473:pathology*; D012169:Retinal Vein / Q000473:pathology; D014603:Uveal Diseases / Q000175:diagnosis / Q000473:pathology; D014792:Visual Acuity