Case report. Progressive systemic sclerosis presenting as interstitial pulmonary fibrosis.
Pulmonary involvement usually is a late manifestation of progressive systemic sclerosis. In the case reported here, dyspnea and pulmonary interstitial fibrosis developed more than a year prior to onset of skin and vascular changes. Open-lung biopsy performed early in the course of the disease failed to yield a definitive diagnosis.
D001706:Biopsy; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D008875:Middle Aged; D011658:Pulmonary Fibrosis / Q000000981:diagnostic imaging* / Q000209:etiology; D011859:Radiography; D012595:Scleroderma, Systemic / Q000150:complications / Q000000981:diagnostic imaging*