[Article in addition to the angioleiomyomatosis of the lungs (author's transl)].
The appearance of a spontaneous chylothorax is a rare case-taking. Chylous effusions are a cardinal symptom of the angioleiomyomatosis of the lungs. Symptomatics and diagnostics of this very rare disease occuring only in women are described by means of one casuistics. Referring to about 60 cases described in literature the probable pathogenetic mechanism and the possibilities of therapy are mentioned in the discussion.
D000328:Adult; D001798:Blood Proteins / Q000032:analysis; D001983:Bronchial Fistula / Q000209:etiology; D002916:Chylothorax / Q000209:etiology; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006222:Hamartoma / Q000473:pathology*; D006801:Humans; D008055:Lipids / Q000097:blood; D008175:Lung Neoplasms / Q000473:pathology*
D001798:Blood Proteins; D008055:Lipids
Beitrag zur Angioleiomyomatose der Lunge.