3-Amino-2-piperidone in the urine of patients with hyperornithinemia.
3-Amino-2-piperidone, a delta-lactam of ornithine, has been detected in the urine of a number of patients with hyperornithinemia. The distinctive yellow colour formed with a ninhydrin-cadmium reagent should help in the detection of hyperornithinemia by urinary chromatography.
D000293:Adolescent; D000328:Adult; D000592:Amino Acid Metabolism, Inborn Errors / Q000652:urine*; D002648:Child; D002852:Chromatography, Ion Exchange; D002854:Chromatography, Paper; D002855:Chromatography, Thin Layer; D004586:Electrophoresis; D005260:Female; D006801:Humans; D007223:Infant; D009952:Ornithine / Q000097:blood*; D010880:Piperidines / Q000652:urine*; D010881:Piperidones / Q000652:urine*
D010880:Piperidines; D010881:Piperidones; D009952:Ornithine