[Congenital tracheobiliary fistula. Report of a case with choledocal hypoplasia (author's transl)].
The authors describe a new observation of a congenital aerobiliar fistula in a newborn infant showing choleptysies associated with a pulmonary obstruction. The most remarkable facts are the presence of a radiological pneumogallbladder, and the existence of a real trifurcation of the trachea on the bronchography, associated with a choledocal hypoplasia. The death having occured before the operation, the autopsy  allowed the confirmation of the termination on the left hepatical duct and the duality of conformation of the fistula, respiratory and biliary. On the occurence of this 9th case, a review of the literature shows the stereotyped nature of the clinical signs and the course of the fistula which seems invariable. The different aspects of the malformation are considered as well as the treatment which necessitates an exeresis by thoracic pathway.
D000015:Abnormalities, Multiple; D000402:Airway Obstruction / Q000209:etiology; D001658:Biliary Fistula / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology; D001995:Bronchography; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D014138:Tracheoesophageal Fistula / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology
Fistule trachéo-biliaire congénitale. A propos d'un cas associé à une hypoplasie du cholédoque.