title: Renal arteriography in von Hippel-Lindau Diease.
abstract: Since 1960, 17 patients with von Hippel-Lindau disease have had cerebellar hemangioblastomas removed at the Victoria General Hospital, Halifax, Nova Scotia. The 4 most recent patients have had renal arteriography as a part of their investigation. Though 3 of these had negative urography, all 4 had positive findings on arteriography. The first patient had bilateral renal cell carcinomas and cysts and failed to respond to 1 year of 'Laetrile' therapy; the second had small cysts in each kidney; the third had bilateral renal cysts, multiple left renal cell carcinomas and a clinically unsuspected right pheochromocytoma; the fourth had a small renal cell carcinoma. It is recommended that all patients with von Hippel-Lindau disease and siblings with any manifestations of the disease have renal arteriography as part of their early investigation.
mesh_terms: D000230:Adenocarcinoma / Q000150:complications / Q000000981:diagnostic imaging; D000328:Adult; D000798:Angiomatosis / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D052177:Kidney Diseases, Cystic / Q000150:complications / Q000000981:diagnostic imaging*; D007680:Kidney Neoplasms / Q000150:complications / Q000000981:diagnostic imaging*; D008297:Male; D010673:Pheochromocytoma / Q000150:complications / Q000000981:diagnostic imaging; D011859:Radiography; D012077:Renal Artery / Q000000981:diagnostic imaging*; D006623:von Hippel-Lindau Disease / Q000150:complications / Q000000981:diagnostic imaging*