[Radiological aspects of diffuse pulmonary lymphangiomyomatosis (author's transl)].
The authors report on 5 cases of diffuse pulmonary lymphangiomyomatosis. This disease occurs in women during the period of genital activity and usually presents with pulmonary signs (9/10) : dyspnoea, pneumothorax, pleural effusion, and hemoptysis. It is also found in association with renal angiomyolipomas and uterine fibromyolipomas. X-ray films of the lungs show : an interstitial syndrome, gas or fluid pleural effusions, and thoracic distention. None of these signs is constant, but the association of an interstitial syndrome with thoracic distention in a young woman appears to be specific for this affection.
D000293:Adolescent; D000328:Adult; D000368:Aged; D005260:Female; D006391:Hemangioma / Q000150:complications; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications; D007889:Leiomyoma / Q000150:complications; D008067:Lipoma / Q000150:complications; D008175:Lung Neoplasms / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology; D008206:Lymphatic Diseases / Q000000981:diagnostic imaging*; D008220:Lymphography; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology; D014594:Uterine Neoplasms / Q000150:complications
Aspects radiologiques de la lymphangiomyomatose pulmonaire diffuse.