Systemic lupus erythematosus and dermatitis herpetiformis: concurrence with Marfan's syndrome.
There is increasing evidence that, as in systemic lupus erythematosus (SLE), deposition of immune complexes plays a role in the pathogenesis of dermatitis herpetiformis (DH). Dermatitis herpetiformis and SLE were diagnosed in a 15-year-old girl with Marfan's syndrome who died of cardiac tamponade secondary to cystic medial necrosis of the ascending aorta. The concurrence of these diseases suggests that predisposition to immune-mediated disorders may be associated with the expression of multiple clinical entities.
D000293:Adolescent; D000936:Antigen-Antibody Complex; D003874:Dermatitis Herpetiformis / Q000150:complications* / Q000276:immunology; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000150:complications*; D008382:Marfan Syndrome / Q000150:complications*
D000936:Antigen-Antibody Complex