[Disorders of sino-atrial and auriculo-ventricular conduction in Steinert's disease. Apropos of one case].
The authors report a case of Steinert's disease with disordered sino-atrial and atrio-ventricular conduction. The presence of sudden syncopal attacks and the absence of a cardiomyopathy (excluded by right- and leftsided haemodynamic studies and coronary arteriography) indicated the insertion of a definitive intra-cavitary pacemaker, especially as the life expectancy of this 54 year old patient did not seem to have been significantly reduced by his disease.
D001283:Atrioventricular Node / Q000503:physiopathology; D006327:Heart Block / Q000628:therapy*; D006329:Heart Conduction System / Q000503:physiopathology*; D006334:Heart Function Tests; D006801:Humans; D008297:Male; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000175:diagnosis / Q000235:genetics / Q000503:physiopathology*; D010138:Pacemaker, Artificial; D011379:Prognosis; D012849:Sinoatrial Node / Q000503:physiopathology; D013575:Syncope / Q000209:etiology; D013577:Syndrome
Troubles de la conduction sino-auriculaire et auriculo-ventriculaire dans la maladie de Steinert. A propos d'un cas