Abdominal cystic lymphangiomatosis: report of a case involving the liver and spleen and illustration of two cases with origin in the greater omentum and root of the mesentery.
B-scan ultrasonic examination of a 10-year-old Mexican-American female with multiple avascular hepatic and splenic defects on both isotopic and angiographic evaluation revealed numerous cystic lesions, a few of which contained numerous internal echoes. Subsequent pathological examination revealed lymphangiomatosis of the liver and spleen. Some of the cysts contained caseous material as predicted only by the ultrasonic examination. Cystic lymphangiomatosis of the spleen is a rare condition and only a few cases of involvement of both the spleen and liver have reported. This is the first such case evaluated by ultrasound. Two cases are also illustrated of cystic lymphangiomatosis with origin in the greater omentum and root of the mesentery.
D000293:Adolescent; D000328:Adult; D002648:Child; D003937:Diagnosis, Differential; D004443:Echinococcosis / Q000175:diagnosis; D005260:Female; D006801:Humans; D008099:Liver / Q000473:pathology; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000473:pathology; D008202:Lymphangioma / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D009852:Omentum; D010534:Peritoneal Neoplasms / Q000175:diagnosis* / Q000473:pathology; D010537:Peritoneum / Q000473:pathology; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis; D013154:Spleen / Q000473:pathology; D013160:Splenic Neoplasms / Q000175:diagnosis* / Q000473:pathology; D014463:Ultrasonography