[Levocardia with ventricular inversion and a single atrium in normal position].
A 12-year child had complete heart block, an abdominal situs inversus with laevocardia. Further investigation demonstrated in addition an inferior vena cava ending into an azygos vein, a shunt at the atrial level and a pulmonary valve stenosis. At operation there was a lone atrium in normal position, a ventricular inversion without transposition of the great vessels. In spite of a corrective operation of the Mustard type, the child died the following day through haemorrhage and low output.
D001344:Autopsy; D006328:Cardiac Catheterization; D002648:Child; D006325:Heart Atria / Q000002:abnormalities; D006327:Heart Block / Q000209:etiology; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D007979:Levocardia / Q000175:diagnosis*; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities; D011666:Pulmonary Valve Stenosis / Q000175:diagnosis; D012857:Situs Inversus / Q000175:diagnosis; D014261:Tricuspid Valve / Q000002:abnormalities; D014682:Vena Cava, Inferior / Q000002:abnormalities
Lévocardie avec inversion ventriculaire et oreillette unique en position normale