Reduced arylsulfatase B activity of the mutant enzyme protein in Maroteaux-Lamy syndrome.
D002478:Cells, Cultured; D002807:Chondroitin / Q000378:metabolism*; D005347:Fibroblasts / Q000201:enzymology; D006801:Humans; D005779:Immunodiffusion; D008099:Liver / Q000201:enzymology; D009083:Mucopolysaccharidoses / Q000201:enzymology*; D009154:Mutation; D012867:Skin / Q000201:enzymology; D013429:Sulfatases / Q000276:immunology / Q000378:metabolism*; D013577:Syndrome
D002807:Chondroitin; D013429:Sulfatases