Development of pulmonary arteriovenous shunt after superior vena cava-right pulmonary artery (Glenn) anastomosis. Report of four cases.
Four patients with cyanotic congenital heart disease who had previously undergone superior vena cava-right pulmonary artery (Glenn) anastomosis developed pulmonary arteriovenous malformations that resulted in significant intrapulmonary right-to-left shunting. This abnormality was documented by selective angiography, oximetry, and contrast echocardiogrphy. It may be a major cause of late clinical deterioration in patients treated with the Glenn anastomosis.
D001164:Arteriovenous Fistula / Q000175:diagnosis* / Q000209:etiology; D002648:Child; D004452:Echocardiography; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011183:Postoperative Complications / Q000175:diagnosis*; D011651:Pulmonary Artery / Q000601:surgery*; D014683:Vena Cava, Superior / Q000601:surgery*