title: [General classification and limited nosology of the phacomatoses].
abstract: The authors suggest a new classification of phacomatoses based on the dysembryoplastic concept of these disorders, which are blastomas of the germ layers. Three main groups are described : ectoblastic, mesoblastic and entoblastic phacomatoses. The diffuse forms are often familial and very evolutive and are contrasted with the regional forms which are commonly sporadic and not very evolutive. The limits of the phacomatoses are finally specified.
mesh_terms: D000798:Angiomatosis / Q000145:classification*; D005855:Germ Layers; D006222:Hamartoma; D006801:Humans; D009456:Neurofibromatosis 1 / Q000145:classification*; D014402:Tuberous Sclerosis / Q000145:classification*
vernacular_title: Classification générale et limites nosologiques des phacomatoses