Multilobular biliary cirrhosis of the liver associated with cystic fibrosis (mucoviscidosis).
A case (including autopsy findings) is reported of multilobular biliary cirrhosis with a strictly nodular liver developing in a 20-year-old male with cystic fibrosis (mucoviscidosis). The pathogenesis of biliary cirrhosis in cystic fibrosis is briefly discussed.
D000328:Adult; D001344:Autopsy; D003550:Cystic Fibrosis / Q000150:complications*; D006801:Humans; D008105:Liver Cirrhosis, Biliary / Q000209:etiology*; D008297:Male