Total anomalous systemic venous drainage.
Total drainage of systemic blood into the left atrium is an exceptional finding in absence of severe intracardiac malformation. In our patient, a boy 3 years and 4 months old, the left superior vena cava, the inferior vena cava, and the coronary sinus drained into the left atrium; there was no right superior vena cava, and the only associated anomaly was a large atrial septal defect. This rare form of cyanotic congenital heart disease was correctly diagnosed and successfully corrected.
D002675:Child, Preschool; D006325:Heart Atria / Q000002:abnormalities; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis; D006801:Humans; D008297:Male; D014682:Vena Cava, Inferior / Q000002:abnormalities*; D014683:Vena Cava, Superior / Q000002:abnormalities*