Anomalies of the intrahepatic portal venous system in congenital hepatic fibrosis.
Duplication of intrahepatic venous channels was observed in 9 of 13 children with congenital hepatic fibrosis and portal hypertension. Portal hypertension due to other causes was not associated with venous duplication. This anomaly may be a distinctive feature of congenital hepatic fibrosis with portal hypertension.
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications; D008099:Liver / Q000098:blood supply*; D008103:Liver Cirrhosis / Q000151:congenital*; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011859:Radiography