[Ultrastructural study of the Dego's disease (report of a new case and literature review) (author's transl)].
An observation of a new case of Degos' disease in a 42 year old woman presenting a merely cutaneous symptomatology, enabled to perform a detailed ultrastructural study of vascular lesions, nerves, infiltrate and perivascular fibroblasts. The episodic clinical evolution with various formation periods of vascular lesions, the frequency of virus-like inclusions in the endothelial cells and fibroblasts, as well as C3 deposits and the presence of intracytoplasmic cylinders in the histiocytes, suggest a common physiopathologic mechanism with the autoimmune diseases. A bibliographic review accompanies the clinico-pathological study.
D000328:Adult; D000367:Age Factors; D001808:Blood Vessels / Q000473:pathology; D002462:Cell Membrane / Q000648:ultrastructure; D003593:Cytoplasm / Q000648:ultrastructure; D004727:Endothelium / Q000473:pathology; D006801:Humans; D008214:Lymphocytes / Q000648:ultrastructure; D009474:Neurons / Q000648:ultrastructure; D009940:Organoids / Q000648:ultrastructure; D012737:Sex Factors; D012867:Skin / Q000098:blood supply / Q000294:innervation; D012871:Skin Diseases / Q000473:pathology*; D013927:Thrombosis / Q000473:pathology*
Ultrastructure de la maladie de Degos (apport d'un nouveau cas et revue de la littérature).