Lymphangiomyomatosis with chylous ascites: treatment with dietary fat restriction and medium chain triglycerides.
Lymphangiomyomyoma is a tumor of lymphatic channels and lymph nodes, clinically manifested by recurrent chylous pleural effusions and ascites. The disease is usually progressive and unresponsive to surgery, chemotherapy, or irradiation. A case of lymphangiomyomatosis in a 24-year-old woman who presented with chylous ascites is described. The patient was treated with dietary fat restriction supplemented with medium chain triglycerides and has remained free of recurrent effusions for 2 years.
D000328:Adult; D001201:Ascites / Q000178:diet therapy* / Q000209:etiology; D002915:Chylous Ascites / Q000178:diet therapy* / Q000209:etiology; D004041:Dietary Fats / Q000627:therapeutic use*; D005260:Female; D006801:Humans; D008202:Lymphangioma / Q000150:complications / Q000178:diet therapy* / Q000473:pathology; D012075:Remission, Spontaneous; D014280:Triglycerides / Q000627:therapeutic use*
D004041:Dietary Fats; D014280:Triglycerides