[Congenital nodular fibromatosis: report of six personal cases (author's transl)].
Six personal cases of nodular congenital fibromatosis are reported: one fibromatosis colli, two fibromas of the fingers one multiple fibromas of the toes and sole associated with osteoporosis and underlying bone lacunes, one recurrent plantar fibromatosis, one disseminated fibromatosis with multiple bone lesions. Such varieties of fibromatosis are very uncommon. Few are isolated such as fibromatosis colli or the fibroma of the fingers. The prognosis is generally good except for the generalized multinodular form which associates a very large visceral involvement. Aetiology is completely unknown. Only few arguments are in favour of an hereditary dominant autosomal transmission of the diffuse multinodular form.
D000293:Adolescent; D001859:Bone Neoplasms / Q000151:congenital* / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D005121:Extremities; D005350:Fibroma / Q000151:congenital* / Q000473:pathology; D006801:Humans; D008297:Male; D012878:Skin Neoplasms / Q000151:congenital*
A propos de la fibromatose nodulaire congénitale (d'après 6 observations).