[Cerebral form of Degos's disease].
The writers report on a new anatomical and clinical observation of Degos' disease with neurological complications. A highly fluctuating meningoencephalitic syndrome took place in a young man 17 years old with a fatal outcome in 2 months. It was a general examination which revealed the lesions of atrophic papulosis typical of the disease. A histological examination confirmed the skin arteriolar, intestinal, and hemispheric lesions. It drew attention to the very abundant similar venular lesions, thus leading to a reconsideration of the physiopathology of this disorder, in which the oft demonstrated autoimmunity and arterial involvement are perhaps only symptoms of the disease.
D000293:Adolescent; D001284:Atrophy; D001927:Brain Diseases / Q000150:complications / Q000209:etiology; D005767:Gastrointestinal Diseases / Q000150:complications; D006801:Humans; D008297:Male; D012871:Skin Diseases / Q000150:complications
Maladie de Degos à forme cérébrale.