[Anomalous pulmonary venous drainage to inferior vena cava (author's transl)].
Four cases between one day of life and seven years are presented. Two of them were males and two females. All of them had cardiac pulsation palpable to the right of the sternum, one with some bulging of the left hemitorax. In two cases a systolic murmur was heard over the second intercostal space associated with fixed splitting of the second sound and the other case presented recurrent infections processes of the lung dying ultimately from bronchoneumonia. On the simple X-ray displacement of the mediastine towards the right side, dextroposition of the heart, right pulmonary hyoplasia, enlargement of the right atrium and image in "scimitar" (obvious in two cases and possibly existed in the other two) was observed. In three cases a lung scan was carried out which showed a marked decrease in perfusion of the right lung. Angiocardiography in all cases as able to demonstrate anomalous venous drainage of the right lung to inferior vena cava directly.
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000818:Animals; D002648:Child; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008168:Lung / Q000000981:diagnostic imaging; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities*; D011859:Radiography; D011877:Radionuclide Imaging; D014684:Venae Cavae / Q000002:abnormalities*
Drenaje anómalo de venas pulmonares derechas a vena cava inferior (síndrome de la cimitarra).