Bilateral keratoconus in Crouzon's syndrome with unilateral acute hydrops.
Bilateral keratoconus was first observed at the age of 13 years in a boy born with Crouzon's syndrome. Corneal hydrops (acute keratoconus) occurred in one of the involved eyes at the age of 15 years. It does not seem that an occurrence of keratoconus in Crouzon's disease has been reported before.
D000015:Abnormalities, Multiple; D000293:Adolescent; D003394:Craniofacial Dysostosis / Q000150:complications*; D003886:Descemet Membrane; D004487:Edema / Q000150:complications; D006801:Humans; D007640:Keratoconus / Q000150:complications*; D008297:Male; D012422:Rupture, Spontaneous