Isolated ventricular discordance and complete atrioventricular canal in situs inversus. Report of successful surgical repair.
Isolated ventricular discordance is a very rare malformation, most often lethal in the first months of life. A patient with this lesion survived to age 9 years in spite of the coexistence of a complete form of atrioventricular (A-V) canal. Surgical repair with a Mustard procedure was associated with correction of the endocardial cushion defect. Situs inversus itself caused no problem. Although permanent complete A-V block occurred, the result has been satisfactory so far. This case is thought to be the first successful correction of this malformation.
D002648:Child; D005260:Female; D006325:Heart Atria / Q000002:abnormalities* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D011183:Postoperative Complications; D012857:Situs Inversus / Q000150:complications* / Q000601:surgery