The conduction system in double outlet right ventricle with subpulmonic ventricular septal defect and related hearts (the Taussig-Bing group).
The Taussig-Bind group of hearts is that group in which the aorta emerges completely from the right ventricle, unrelated to the position of the ventricular septal defect (VSD), while the pulmonary trunk emerges at varying degrees from the right ventricle related to the location of the VSD. Several types of surgical procedures involve the VSD in these hearts. The conduction systems in six of these hearts were therefore studied. The atrioventricular (A-V) bundle lies in the inferior (posterior) wall of the defect on the left side beneath the summit of the ventricular septum. In some cases, the bundle may be proximal to the defect, thus lying intramuscularly, and only the right and left bundle branches are related to the defect. The pattern od development of the atrioventricular (A-V) node, bundle and bundle branches is related primarily to the development of the endocardial cushions and posterior ventricular septum, and not to that of the absorption of the bulbus.
D001011:Aorta / Q000473:pathology; D001017:Aortic Coarctation / Q000473:pathology; D001283:Atrioventricular Node / Q000473:pathology; D002036:Bundle of His / Q000473:pathology; D002648:Child; D004374:Ductus Arteriosus, Patent / Q000473:pathology; D005260:Female; D006329:Heart Conduction System / Q000473:pathology; D006330:Heart Defects, Congenital / Q000473:pathology*; D006345:Heart Septal Defects, Ventricular / Q000473:pathology*; D006346:Heart Septum / Q000473:pathology; D006351:Heart Valves / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities / Q000473:pathology; D012849:Sinoatrial Node / Q000473:pathology; D013577:Syndrome; D014188:Transposition of Great Vessels / Q000473:pathology*