[Angioimmunoblastic adenopathies].
Angio-lymphoblastic lymphadenopathies are a newly described haematological entity, though not rare, characterised by a histological triad (vascular neogenesis, highly polymorphic or predominantly immunoblastic cellular proliferation and the presence of acidophilic protein deposits), a clinical syndrome consisting essentially of voluminous disseminated lymphadenopathy and hepatosplenomegaly and abnormal laboratory findings dominated by a polyclonal dysproteinaemia. This disorder, the first four French cases of which are described here, does not appear to be malignant in its early stages and is sensitive to corticosteroid therapy at that time. Secondary sarcomatous transformation is  possible.
D000328:Adult; D000368:Aged; D002471:Cell Transformation, Neoplastic; D003937:Diagnosis, Differential; D004406:Dysgammaglobulinemia / Q000175:diagnosis / Q000276:immunology* / Q000473:pathology; D005260:Female; D006529:Hepatomegaly / Q000209:etiology; D006801:Humans; D006942:Hypergammaglobulinemia / Q000175:diagnosis / Q000276:immunology / Q000473:pathology; D007153:Immunologic Deficiency Syndromes / Q000276:immunology*; D008198:Lymph Nodes / Q000473:pathology; D008206:Lymphatic Diseases / Q000175:diagnosis / Q000276:immunology* / Q000473:pathology; D008297:Male; D008875:Middle Aged; D012509:Sarcoma / Q000175:diagnosis; D013163:Splenomegaly / Q000209:etiology
Les adénopathies angio-immunoblastiques