Leukocyte peroxidase in Spielmeyer-Vogt's disease.
Leukocyte peroxidase activity was estimated in 5 patients with the juvenile form of neuronal ceroid lipofuscinosis (Spielmeyer-Vogt's disease) and in 15 healthy controls. In contradiction to recent reports normal activity of p-phenylene diamine mediated peroxidase was found in the patients. The possible role of contamination of the white cell preparation with hemoglobin is discussed.
D000293:Adolescent; D000328:Adult; D002374:Catalase / Q000097:blood; D002566:Ceroid / Q000032:analysis; D004912:Erythrocytes / Q000201:enzymology; D005189:False Positive Reactions; D005260:Female; D005979:Glutathione Peroxidase / Q000097:blood; D006801:Humans; D007962:Leukocytes / Q000201:enzymology*; D008064:Lipidoses / Q000201:enzymology*; D008062:Lipofuscin / Q000097:blood*; D008297:Male; D010544:Peroxidases / Q000097:blood*; D010860:Pigments, Biological / Q000097:blood*
D002566:Ceroid; D008062:Lipofuscin; D010860:Pigments, Biological; D010544:Peroxidases; D002374:Catalase; D005979:Glutathione Peroxidase