[Multiple angioleiomyomas of both lungs. Probable hamartomatous tumors. Very late death due to respiratory insufficiency].
Case presentation : Multiple tumor nodules in both lungs, identified by biopsy and necropsy, in a 48 year old woman, 8 years after radiological discovery ; death due to respiratory failure after long tolerance ; peculiar angio-leiomyomatous type pulmonary tumors. This purely pulmonary tumor disease is difficult to understand ; the most probable hypothesis envisaged is that of hamartomatosis ; comparison with certain general dysplastic disease is possible, and in particular Bourneville's disease and lymphangio-myomatosis.
D000328:Adult; D005260:Female; D006222:Hamartoma / Q000150:complications / Q000175:diagnosis*; D006391:Hemangioma / Q000150:complications / Q000175:diagnosis*; D006801:Humans; D007889:Leiomyoma / Q000150:complications / Q000175:diagnosis*; D008168:Lung / Q000473:pathology; D008175:Lung Neoplasms / Q000150:complications / Q000175:diagnosis*; D012131:Respiratory Insufficiency / Q000209:etiology
Angio-léiomyomes multiples des 2 poumons. Tumeurs hamartomateuses probables. Décès très tardif par insuffisance respiratoire