[Idiopathic intestinal lymphangiectasis. Evolution with M.C.T. (author's transl)].
A case of idiopathic intestinal lymphangiectasis is reported in a three month old child. Clinical course and laboratory findings are given in relation to administration of three diets containing different concentrations and types of fat. Short term improvement was only noticed with diets containing low concentrations of long chain triglycerides supplement with medium chain triglycerides. Clinical manifestations related to fat malabsortion improved greatly but there was no relationship with serum protein level. No effect on low level of gamma-globulins and lymphatic displasia was found as sawn in an intestinal biopsy performed after three months of treatment. Nevertheless, long-term results were poor and only were evident in a diminution of steatorrhea and normalization of stools.
D004041:Dietary Fats / Q000627:therapeutic use; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007232:Infant, Newborn, Diseases / Q000178:diet therapy*; D008201:Lymphangiectasis, Intestinal / Q000178:diet therapy*; D008297:Male; D008722:Methods; D011504:Protein-Losing Enteropathies / Q000178:diet therapy*; D014280:Triglycerides / Q000627:therapeutic use
D004041:Dietary Fats; D014280:Triglycerides
Linfangiectasia intestinal idiopática. Evolución con triglicéridos de cadena media