Systemic mastocytosis--central nervous system features and lymphographic demonstration of lymph node involvement.
Systemic mastocytosis is uncommon. A patient is reported with many of the characteristic lesions of this disorder but with two features not before described--the occurrence of mixed pyramidal and neuromyopathic neurological signs and the demonstration of lymph nodes with abnormal architecture by lymphography.
D005260:Female; D006529:Hepatomegaly / Q000150:complications; D006801:Humans; D008198:Lymph Nodes / Q000000981:diagnostic imaging*; D008875:Middle Aged; D009461:Neurologic Manifestations; D011859:Radiography; D013163:Splenomegaly / Q000150:complications; D014582:Urticaria Pigmentosa / Q000150:complications* / Q000000981:diagnostic imaging