title: [Primary interstitial pneumopathies].
abstract: Primitive interstitial pneumopathies are only a temporary classification. They seem to be due to an evolution for the worse of a "diffuse alveolar damage" of unknown origin. Evolution towards pulmonary fibrosis and respiratory insufficiency is their common risk. Etiopathogenic hypotheses would favour the immunological etiology. A diagnosis of primitive interstitial pneumopathy is reached by elmination when no known cause can be found. Liebow's classification remains valuable for pathology but is debatable where anatomo-clinical correlations, etiological hypotheses and the eventual effect of treatment are concerned. Today these primitive forms still represent 40% of the interstitial lung diseases, the causes of which are progressively discovered.
mesh_terms: D000305:Adrenal Cortex Hormones; D006801:Humans; D008264:Macrophages; D008854:Microscopy, Electron; D010503:Periodic Acid-Schiff Reaction; D010950:Plasma Cells; D011379:Prognosis; D011650:Pulmonary Alveoli / Q000473:pathology; D011658:Pulmonary Fibrosis / Q000145:classification / Q000175:diagnosis / Q000209:etiology / Q000473:pathology
chemical_list: D000305:Adrenal Cortex Hormones
vernacular_title: Les pneumopathies interstitielles primitives