Lymphangiomatosis with splenic involvement.
Severe splenomegaly and anemia developed in a 5-year-old girl with diffuse lymphangiomatosis of the upper part of the body. Radioisotope scanning and celiac angiography demonstrated lymphangiomatosis of the spleen, a rare but diagnosable condition. Intractable infection in areas of ulcerated skin led to her death from overwhelming sepsis.
D000740:Anemia / Q000175:diagnosis; D002675:Child, Preschool; D004604:Elephantiasis / Q000175:diagnosis; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008202:Lymphangioma / Q000000981:diagnostic imaging / Q000473:pathology; D011859:Radiography; D013154:Spleen / Q000473:pathology; D013160:Splenic Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology; D013163:Splenomegaly / Q000000981:diagnostic imaging