The liver in hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu disease).
The livers of four patients with hereditary hemorrhagic telangiectasia--including the original case of Osler--were examined at autopsy. Characteristic random focal fibrovascular lesions were found in all. The importance of recognizing the apparently common and seemingly benign hepatic involvement in this disease is emphasized in view of its possible confusion with more serious types of liver disease that may complicate the condition.
D000368:Aged; D001344:Autopsy; D002277:Carcinoma / Q000150:complications; D003238:Connective Tissue / Q000473:pathology; D004844:Epistaxis / Q000150:complications; D005260:Female; D006331:Heart Diseases / Q000150:complications; D006391:Hemangioma / Q000150:complications; D006801:Humans; D008099:Liver / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D013274:Stomach Neoplasms / Q000150:complications; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications / Q000235:genetics / Q000473:pathology*