Osteogenesis imperfecta. Review of the medical and dental literature and report of a case.
Osteogenesis imperfecta is a rare congenital bone disease affecting the mesenchyme and some of its derivatives resulting in three basic clinical entities--fragility of bones, blue sclera, and otosclerosis. The medical and dental literature pertaining to osteogenesis imperfecta is reviewed, and a specific dental case is discussed.
D002648:Child; D006801:Humans; D008297:Male; D010013:Osteogenesis Imperfecta / Q000150:complications* / Q000209:etiology / Q000473:pathology; D014076:Tooth Diseases / Q000209:etiology*