title: Anaesthesia for portocaval bypass in patients with metabolic diseases.
abstract: The biochemical lesions of the glycogen storage diseases and of familial hyperlipidaemia are discussed and the anaesthetic management of patients with these conditions, for the procedure of portocaval bypass, is described.
mesh_terms: D000768:Anesthesia, General; D055598:Chemical Phenomena; D002621:Chemistry; D002648:Child; D002675:Child, Preschool; D004737:Enflurane; D005260:Female; D006008:Glycogen Storage Disease / Q000378:metabolism / Q000628:therapy*; D005953:Glycogen Storage Disease Type I / Q000628:therapy; D006221:Halothane; D006801:Humans; D006949:Hyperlipidemias / Q000235:genetics / Q000628:therapy; D007263:Infusions, Parenteral; D008297:Male; D008661:Metabolism, Inborn Errors / Q000628:therapy*; D009609:Nitrous Oxide; D011167:Portacaval Shunt, Surgical; D011229:Preanesthetic Medication
chemical_list: D004737:Enflurane; D009609:Nitrous Oxide; D006221:Halothane