title: [Threedimensional cephalometric contribution to the study of mandibulo-facial dysplasias].
abstract: The cephalometric particulars of the dysplastic syndrome of the first visceral segment, the dysostosis mandibulofacialis Franceschetti-Zwahlen were investigated. Ten patients were found with the identical symptom of a typical, uni- or bilateral microtia of the external ear. The cephalometric characteristics of the syndrome may be summarized as follows: - retroposition of the middle face - retroposition of maxilla and mandible - retrorotation of the mandible - reduction of vertical and lateral dimension of the face - reduction of transverse diameter of both dental arches - shortened mandibular base - both halves of the face are affected, but more so the half with microtia - the chin is deflected toward the affected side. Most of these symptoms must be attributed to disturbed organogenesis. With the rest of them, functional adaptation cannot be exluded.
mesh_terms: D000293:Adolescent; D002508:Cephalometry / Q000379:methods*; D002648:Child; D006801:Humans; D008297:Male; D008342:Mandibulofacial Dysostosis / Q000000981:diagnostic imaging*; D008445:Maxillofacial Development; D011859:Radiography; D012886:Skull / Q000000981:diagnostic imaging
vernacular_title: Contribution céphalométrique tridimensionnelle à l'étude des dysplasies mandibulo-faciale