Total sequestration of the right lung.
A 2-day-old baby with severe respiratory distress and cyanosis was admitted to the hospital with a totally opacified right pleural cavity. Preoperative studies demonstrated absence of the right pulmonary artery, and a patent ductus arteriosus, and a left pulmonary artery pressure of 85/45 mm. Hg. The hypoplastic right lung received its entire blood supply from multiple vessels through the diaphragm. The infant's condition improved initially after a right pneumonectomy, but she died of progressive respiratory insufficiency at the age of 7 months.
D001998:Bronchopulmonary Sequestration / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D006328:Cardiac Catheterization; D002932:Cineangiography; D004374:Ductus Arteriosus, Patent / Q000150:complications; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications; D006801:Humans; D007231:Infant, Newborn; D011013:Pneumonectomy; D011651:Pulmonary Artery / Q000002:abnormalities