title: [Congenital complete atrio-ventricular block].
abstract: Case-histories and ECG of 23 patients with congenital atrio-ventricular heart block were studied. Most of these were up to 14 years old. In 10 of these patients concomitant congenital cardiac defects were uncovered which in 7 cases were combined with a corrected transposition of the major vessels. A relationship between the localization of the ventricular pacemaker and the clinical picture of the disease. The attacks of the Morgagni-Adams-Stocks disease were, as a rule, observed in patients with the ventricular pacemaker located beneath the bundle of His bifurcation, which manifested itself on the ECG by deformation and broadening of the QRS complex in the form of a complete or incomplete block of one or both of the bundle of His crura. Most patients with circulatory insufficiency suffered from severe concomitant congential cardiac failures or from frequent attacks of the Morgagni-Adams-Stocks disease.
mesh_terms: D000219:Adams-Stokes Syndrome / Q000150:complications; D000293:Adolescent; D000328:Adult; D001022:Aortic Valve Insufficiency / Q000150:complications; D002648:Child; D002675:Child, Preschool; D004374:Ductus Arteriosus, Patent / Q000150:complications; D004562:Electrocardiography; D005260:Female; D006327:Heart Block / Q000150:complications / Q000151:congenital* / Q000175:diagnosis; D006345:Heart Septal Defects, Ventricular / Q000150:complications; D006801:Humans; D008297:Male; D008946:Mitral Valve Stenosis / Q000150:complications; D011651:Pulmonary Artery; D014188:Transposition of Great Vessels / Q000150:complications
vernacular_title: Vrozhdennaia polnaia atrio-ventrikuliarnaia blokada serdtsa