Radical surgical treatment of esophageal stenosis due to epidermolysis bullosa.
Stenotic lesions of the esophagus in epidermolysis bullosa are a rare cause of dysphagia. Even though 50 cases have been reported in the literature, only recently has surgical treatment been suggested for these patients. In our patients, who had an annular stenosis just distal to the pharyngoesophageal juncture, resection of a mucosal cylindrical segment with reanastomosis through a longitudinal esophageal myotomy was successful. This method of treatment is suggested for patients in whom the stenosis is localized.
D000328:Adult; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D004935:Esophageal Diseases / Q000150:complications*; D004940:Esophageal Stenosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D011859:Radiography