title: Ultrastructural findings in incontinentia pigmenti.
abstract: From their ultrastructural study of incontinenti pigmenti, the authors confirm that in this condition there is no pigmentary anomaly, but that pigmentation is the last step of a still unknown process. At birth those who are affected display an intracellular edema which leads to the formation of a vesocobulla. In all 3 stages, the epidermis shows dyskeratotic cells and a transient pigmentary discharge.
mesh_terms: D000015:Abnormalities, Multiple / Q000473:pathology*; D001768:Blister / Q000473:pathology; D002467:Cell Nucleus / Q000648:ultrastructure; D003896:Desmosomes / Q000648:ultrastructure; D004487:Edema / Q000473:pathology; D004804:Eosinophils / Q000648:ultrastructure; D005128:Eye Diseases / Q000473:pathology; D006644:Histiocytes / Q000648:ultrastructure; D006801:Humans; D007633:Keratins; D008407:Mast Cells / Q000648:ultrastructure; D008543:Melanins; D008544:Melanocytes / Q000648:ultrastructure; D008854:Microscopy, Electron; D008933:Mitochondrial Swelling; D009508:Nevus, Pigmented / Q000473:pathology; D010587:Phagocytosis; D010859:Pigmentation Disorders / Q000473:pathology*; D013577:Syndrome
chemical_list: D008543:Melanins; D007633:Keratins