Juvenile aponeurotic fibroma. Report of three cases and a review of the literature.
Three cases of a distinctive soft tissue fibrous tumor with spotty calcification demonstrate the lesion originally described by Keasby as Juvenile Aponeurotic Fibroma. The tumor tends to occur on the volar surface of the hands and feet in children and adolescents but may be seen in other areas in all age groups. Size rarely exceeds 3.0 cm. The tumors are fixed to the fascial layers. In previously reported patients pain was not described as an important factor, but both pain and tenderness were striking in all 3 of our cases. Microscopically the dominant feature is a fribrous stromal pattern of fusiform cells with inclusions of mast cells. Spotty calcification is a constant finding and appears to increase with duration of tumor. Local recurrence after excision and an aggressive histologic appearance may raise the question of malignancy. However, neither destruction of normal tissue surrounding the tumor nor metastases have occurred. Local exicision is the treatment of choice.
D000293:Adolescent; D001706:Biopsy; D004550:Elbow / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D005350:Fibroma / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D005528:Foot / Q000000981:diagnostic imaging / Q000473:pathology; D005534:Foot Diseases; D006801:Humans; D008297:Male; D011859:Radiography