Right-to-left interatrial shunting with normal right ventricular pressure. A puzzling haemodynamic picture associated with some rare congenital malformations of the right ventricle and tricuspid valve.
Haemodynamic and angiographic findings are described in 5 cases with rare anomalies of the right ventricle and the second there was isolated congenital 'absence' of the tricuspid valve. The remaining 3 cases all had isolated congenital hypoplasia of the right ventricle; in 2 of these 3 cases closure of the atrial septal defect was successful in abolishing cyanosis and symptoms,while the third is awaiting surgical correction.
D000792:Angiography; D001794:Blood Pressure; D006328:Cardiac Catheterization; D002648:Child; D002675:Child, Preschool; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging; D006344:Heart Septal Defects, Atrial / Q000503:physiopathology* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D014261:Tricuspid Valve / Q000002:abnormalities*