[Congenital hypoplasia of the right ventricular myocardium (Uhl's anomaly)].
Partial aplasia of the right ventricular myocardium (Uhl's anomaly) was found at post-mortem examination of a 71-year-old woman. Most of the cases of this anomaly end fatally, in infancy or childhood, with treatment-resistant right heart failure, the diagnosis being only rarely made in life.
D000368:Aged; D000792:Angiography; D001344:Autopsy; D006328:Cardiac Catheterization; D004562:Electrocardiography; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D010138:Pacemaker, Artificial; D013577:Syndrome
Die Uhlsche Krankheit