Gorlin's syndrome.
The uncommon familial syndrome of multiple odontogenic keratocysts, basal cell naevi and skeletal anomalies is reviewed, and seven cases are described, including one patient who developed squamous cell carcinoma in a previous odontogenic keratocyst of the maxilla. We wish to thank Consultants from the Royal National Throat, Nose and Ear Hospital, The Middlesex Hospital and the Eastman Dental Hospital, who allowed us access to their patients; Mr. D. Garfield Davies, Dr. M. F. Spittle, Mr. D. Winstock, Mr. H. P. Cook, Professor H. C. Killey and Mr. L. W. Kay. We are grateful to Professor L. Michaels and Mr. D. J. Connolly for preparation of the illustrations and to Mrs. A. Matthews for the typescript.
D000077:Acetabulum / Q000473:pathology; D000293:Adolescent; D000328:Adult; D001845:Bone Cysts / Q000000981:diagnostic imaging / Q000473:pathology; D002114:Calcinosis; D002280:Basal Cell Carcinoma / Q000473:pathology / Q000532:radiotherapy; D002294:Carcinoma, Squamous Cell / Q000209:etiology; D002648:Child; D002971:Cleft Lip / Q000601:surgery; D005260:Female; D006801:Humans; D007223:Infant; D007571:Jaw Diseases; D008297:Male; D008441:Maxillary Neoplasms / Q000209:etiology; D011859:Radiography; D012272:Ribs / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012877:Skin Manifestations; D012878:Skin Neoplasms / Q000532:radiotherapy / Q000601:surgery; D012886:Skull / Q000000981:diagnostic imaging; D013577:Syndrome