[Involvement of nonhypothalamic encephalic structures in the Hand-Schüller-Christian disease. Report of a case and review of the literature].
A case of Hand-Schüller-Christian disease which presented a pyramidal syndrome besides elements of the classical triad and concentric retraction of the visual field is reported. The rare involvement of non-hypothalamic encephalic structures in that disease is emphasized together with the favourable effect of corticotherapy and radiotherapy.
D000293:Adolescent; D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D001932:Brain Neoplasms / Q000209:etiology / Q000532:radiotherapy / Q000628:therapy; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000628:therapy; D006801:Humans; D008297:Male; D009461:Neurologic Manifestations
D000305:Adrenal Cortex Hormones
Comprometimento de estruturas encefalicas não hipotalamicas na molestia de Hand-Schüller-Christian. Relato de caso e revisão da literatura