[The pathology and clinical features of generalized lymphangiomyomatosis (author's transl)].
Generalized lymphangiomyomatosis with diffuse pulmonary involvement was diagnosed at post-mortem of a 26-year-old woman. The disease occurs only in women, during or after their reproductive phase, with chylous effusion, especially chylothorax, dyspnoea and chronic progression. It is a multitopic condition starting with a focal lesion, which has its origin in the smooth musculature of the lymphatics and probably develops in dependence on hormonal factors.
D000328:Adult; D000367:Age Factors; D002916:Chylothorax / Q000150:complications; D004417:Dyspnea / Q000150:complications; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis* / Q000209:etiology; D008202:Lymphangioma / Q000150:complications / Q000175:diagnosis* / Q000209:etiology; D009130:Muscle, Smooth; D012737:Sex Factors
Zur Pathologie und Klinik der generalisierten Lymphangiomyomatose