[Unusual combination of absence of the left pulmonary artery and homolateral malformation of the kidney and ureter (author's transl)].
In an one year old asymptomatic girl with a slight levoposition of the heart on chest X-ray and mild right ventricular hypertrophy in the ECG further cardiological investigation disclosed several anomalies: Absence of the left pulmonary artery, collateral vessels to the left lung both from the abdominal aorta and from a left brachiocephalic trunc, hypoplasia of the left lung, right sided aortic arch. There was no malformation of the heart itself. This is supposed to be the first reported case, in which the aforementioned anomalies were associated with hypoplasia and hydronephrosis of the left kidney and stenosis of the ostium on the left ureter. Considering the normal and pathologic development of the human embryo it may be assumed, that there is no immediate relationship between the malformation of the left lung and its vessels on one hand and the defects of the left kidney and ureter on the other hand. The hypothesis is put forward, that the damage of the embryo occurred limited to one side during the period of teratogenetic determination common to both of the organ systems involved.
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D006869:Hydronephrosis / Q000150:complications; D007223:Infant; D007668:Kidney / Q000002:abnormalities*; D011651:Pulmonary Artery / Q000002:abnormalities*; D011859:Radiography; D012077:Renal Artery / Q000002:abnormalities; D014513:Ureter / Q000002:abnormalities*
Ungewöhnliche Kombination einer linksseitigen Pulmonalarterienagenesie mit einer homolateralen Fehlbildung der Niere und des Ureters