Subcellular distribution and cofactor function of human branched chain alpha-ketoacid dehydrogenase in normal and mutant cultured skin fibroblasts.
D002478:Cells, Cultured; D002648:Child; D002675:Child, Preschool; D005260:Female; D005347:Fibroblasts / Q000201:enzymology; D006801:Humans; D007223:Infant; D007651:Keto Acids; D007700:Kinetics; D008297:Male; D008566:Membranes / Q000032:analysis; D008928:Mitochondria / Q000201:enzymology; D009154:Mutation; D010088:Oxidoreductases / Q000032:analysis* / Q000378:metabolism; D011768:Pyruvate Dehydrogenase Complex / Q000032:analysis; D012867:Skin / Q000201:enzymology*; D013347:Subcellular Fractions / Q000201:enzymology
D007651:Keto Acids; D011768:Pyruvate Dehydrogenase Complex; D010088:Oxidoreductases