[Agenesia of the pulmonary valves manifested by ventilation disorders. In the newborn].
Agenesia of the pulmonary valves is often responsible for severe disorders of ventilation by bronchial compression in newborns. This may be involved in case of respiratory distress, with a double murmur, expressing the stenosis of an avalvulated pulmonary ring and the massive pulmonary regurgitation. The bad tolerance is due to the association with an interventricular dilatation of the pulmonary artery, which characterizes this malformative complex. The prognosis is severe and the treatment is disappointing since all surgical attempts failed at this age.
D000402:Airway Obstruction / Q000209:etiology*; D000783:Aneurysm / Q000209:etiology; D001238:Asphyxia Neonatorum / Q000209:etiology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities*
Agenesie des valves pulmonaires revelee par des troubles de ventilation. Chez le nouveau-ne