[A persistent craniopharyngeal canal combined with a meningoencephalocele (author's transl)].
The anatomical and embryological facets of the persistent craniopharyngeal canal combined with a meningoencephalocele are reviewed, and the case of a 6 year old girl is reported. Postnatal dyspnea and cyanosis improved after perforation of nasopharyngeal cyst, and adenoidectomy was performed at the age of 8 months. The second episode of meningitis led to its radiological assessment and correct diagnosis. Surgical treatment is limited because the location of the pituitary in this child is not known.
D000233:Adenoidectomy; D002648:Child; D003560:Cysts / Q000601:surgery; D003638:Deafness / Q000601:surgery; D004677:Encephalocele; D005260:Female; D006801:Humans; D008416:Mastoid / Q000601:surgery; D008588:Meningocele; D010608:Pharyngeal Diseases / Q000601:surgery; D010614:Pharynx / Q000002:abnormalities*; D011011:Pneumoencephalography; D012658:Sella Turcica / Q000000981:diagnostic imaging; D012886:Skull / Q000002:abnormalities*; D013064:Speech Disorders / Q000209:etiology; D013100:Sphenoid Bone / Q000002:abnormalities*
Offener Canalis cranio-pharyngeus mit spheno-pharyngealer Meningoenzephalozele