[Treatment of extreme obesity in a case of Prader-Willi-Labhart-syndrome (author's transl)].
A boy 14 years of age, weighing 93,45 kg and 143 cm in height was refered to our clinic with hyperphagia and pain in the joints. The patient showed the Prader-Labhart-Willi-syndrome. Through maximal diet therapy, 2 admittances in our ward and through intensive psychological outpatient care, we have seen a weight loss of 26 kg in 18 months and clear improvement in the patient's health. We would like to draw attention to the fact that a weight reduction diet is a cooperative family effort. To satiate uncontrollable hunger an intermittent dose of Fenfluramine (0,5 mg/kg) is recommended.
D000293:Adolescent; D002239:Carbohydrate Metabolism, Inborn Errors / Q000178:diet therapy*; D005277:Fenfluramine / Q000627:therapeutic use; D006801:Humans; D006965:Hyperplasia / Q000175:diagnosis; D008607:Intellectual Disability / Q000628:therapy; D008297:Male; D008661:Metabolism, Inborn Errors; D009765:Obesity / Q000175:diagnosis / Q000178:diet therapy*; D011613:Psychotherapy
D005277:Fenfluramine
Behandlung der exzessiven Adipositas am Beispiel des Prader-Willi-Labhart-Syndroms