Scleroderma heart disease with slow flow velocity in coronary arteries.
A young woman with scleroderma heart disease is presented. Complete work-up including hemodynamic studies revealed biventricular dysfunction, left ventricular hypokinesia and normal coronary arteries with slow flow velocity in coronary arteries. This finding, though not diagnostic, is consistent with small vessels disease secondary to scleroderma. Favorable prognosis in our patient on medical management is encouraging. No conclusions can be drawn on the basis of one patient. Further work is warranted in scleroderma patients with cardiomegaly to define the status of the myocardial microcirculation and its possible role in their prognosis.
D000328:Adult; D001783:Blood Flow Velocity; D003331:Coronary Vessels / Q000503:physiopathology*; D004562:Electrocardiography; D005260:Female; D006331:Heart Diseases / Q000175:diagnosis / Q000503:physiopathology*; D006352:Heart Ventricles / Q000000981:diagnostic imaging; D006801:Humans; D010701:Phonocardiography; D011859:Radiography; D012595:Scleroderma, Systemic / Q000175:diagnosis / Q000503:physiopathology*; D014672:Vectorcardiography