[Sclerodermoid porphyria cutanea tarda associated with cataract].
Two cases of Porphyria cutanea tarda with sclerodermoid changes associated with cataracta are studied. Far from being considered as an authentic scleroderma, the sclerodermoid aspect, very common in patients with Porphyria cutanea tarda, seems to represent one among the many residual alterations of the precocious cutaneous senescence, peculiar to these individuals hypersensitive to luminic radiations. The first patient had familial cases of cataracta. The second had no familial occurrence of it. The association of cataracta and Porphyria cutanea tarda, for the first time mentioned in the literature, would be one complication to be added to this very polymorphous syndrome.
D000328:Adult; D000368:Aged; D002386:Cataract / Q000150:complications*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D011164:Porphyrias / Q000150:complications* / Q000473:pathology; D012595:Scleroderma, Systemic / Q000150:complications* / Q000473:pathology; D012877:Skin Manifestations
Porfiria cutánea tarda esclerodermiforme, asociada com catarata