Congenital hepatic fibrosis.
During 10 years four patients with congenital hepatic fibrosis were seen in a general hospital in London; three presented in adult life. It is suggested that the condition may account for a larger proportion of patients with chronic liver disease than has been thought to be the case.
D000293:Adolescent; D000328:Adult; D000367:Age Factors; D004381:Duodenal Ulcer / Q000150:complications; D006529:Hepatomegaly / Q000150:complications; D006801:Humans; D007674:Kidney Diseases / Q000150:complications; D008099:Liver / Q000473:pathology; D008103:Liver Cirrhosis / Q000151:congenital* / Q000473:pathology; D008297:Male; D013163:Splenomegaly / Q000150:complications