[Case report of a primary pericollagen amyloidosis (author's transl)].
The authors report about a female patient, 59 years old, who was suffering from a stenosis of the cardia. A malignant process was suspected and an operative treatment was planed. During the preoperative internal examinations a low voltage in the ECG was found so that an amyloidosis was suspected. This was proved by biopsy of the mucosa of the rectum. A chronic suppurative disease could not be found, it was then assumed that the patient is suffering from a "primary pericollagen amyloidosis". Because a splitting of the stenosis through the esophagoscope the biopsy showed no malignancy, but congo-red positive material around collagen tissue. This seldom disease, the differential-diagnosis and the possibilities of treatment are discussed. Under symptomatic therapy the patient is doing well 2 years since.
D000686:Amyloidosis / Q000097:blood / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D001706:Biopsy; D002299:Cardia; D003327:Coronary Disease / Q000150:complications / Q000209:etiology; D003937:Diagnosis, Differential; D004931:Esophageal Achalasia / Q000209:etiology / Q000628:therapy; D004943:Esophagogastric Junction / Q000473:pathology; D004947:Esophagus / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008875:Middle Aged; D011859:Radiography; D012007:Rectum / Q000473:pathology; D013272:Stomach Diseases / Q000175:diagnosis; D013274:Stomach Neoplasms / Q000175:diagnosis; D014135:Tracheal Stenosis / Q000209:etiology; D014525:Urethral Stricture / Q000209:etiology / Q000628:therapy
Zur klinischen Diagnose der primär perikollagenen Amyloidose