[Proliferation of the transverse tubular system during a tardive and familial myopathy].
The authors report a case of non-progressive, late-onset, recessive, sex-linked myopathy. Electron microscopy reveals a striking proliferation of the T system. This proliferation might be interpreted as indicating an abortive attempt of muscle to regenerate, which could explain the clinical course. Some basic ultrastructural aspects concerning the T system are reported. The signification of the findings of numerous "zebra bodies" is discussed.
D000328:Adult; D006801:Humans; D008297:Male; D008870:Microtubules / Q000648:ultrastructure*; D009132:Muscles / Q000648:ultrastructure*; D009135:Muscular Diseases / Q000235:genetics* / Q000473:pathology
Prolifération du système tubulaire transversal au cours d'une myopathie tardive et familiale