[Hemochromatosic cardiomyopathy. Report of a case with registration of his bundle potentials and hemodynamic examination (author's transl)].
A case of idiopathic haemochromatosis in a young adult aged 23, with pre-eminent cardiac symptoms is described. The cardiac symptoms consisted of heart failure and various types of arrhythmias (atrial and ventricular tachycardia, AV block). The haemodynamic studies revealed a biventricular diastolic hypertension; the cineangiocardiography showed a diffuse hypokinesis of the left ventricle and mitral regurgitation.
D000328:Adult; D002036:Bundle of His / Q000503:physiopathology*; D009202:Cardiomyopathies / Q000175:diagnosis* / Q000503:physiopathology; D006329:Heart Conduction System / Q000503:physiopathology*; D006333:Heart Failure / Q000209:etiology; D006432:Hemochromatosis / Q000150:complications* / Q000503:physiopathology; D006439:Hemodynamics; D006801:Humans; D008297:Male; D008944:Mitral Valve Insufficiency / Q000209:etiology; D013610:Tachycardia / Q000209:etiology
Miocardiopatia emocromatosica. Descrizione di un caso con registrazione dei potenziali del fascio di His ed esame emodinamico