[Sturge-Weber syndrome: apropos of an anatomo-clinical case report with prepapillary glial proliferation].
The authors report the case of a woman with Sturge-Weber syndrome (oculotrigeminate form) presenting with neovascular glaucoma of abrupt onset during pregnancy. Since medical treatment failed, she underwent a retrobulbar alcoholisation. Three months after delivery, enucleation was performed for esthetic reasons. The enucleated eye showed diffuse choroidal angioma, total retinal detachment and a prepapillary glial proliferation. We discuss this uncommon association.
Kallay
O
O
Service d'Ophtalmologie, Cliniques Universitaries St-Luc, Bruxelles, Belgique.
Boucquey
D
D
Maes
E
E
Brucher
J M
JM
D000328:Adult; D002830:Choroid Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D015353:Eye Enucleation; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D012163:Retinal Detachment / Q000473:pathology; D013341:Sturge-Weber Syndrome / Q000175:diagnosis / Q000473:pathology*
Syndrome de Sturge-Weber: à propos d'une observation anatomo-clinique avec prolifération gliale prépapillaire.