title: [14 cases of communicating syringomyelia associated with Chiari I malformation in children].
abstract: The authors review their experience of 14 children with syringomyelia and associated Chiari I malformation observed during the last 21 years. Initial symptoms were motor weakness (57%), sensory signs (50%), scoliosis (50%) and bladder dysfunction (21.5%), while signs of admission were pyramidal signs (78.5%) with motor deficit (43%), spinal deformities (64.2%), syringomyelic syndrome (36%) and sensory deficit (21.5%). Four children were investigated with myelography, three with myelography and spinal CT Scan and the last seven cases with MRI. Ten children (71.4%) underwent a decompression of the Chiari malformation with or without drainage of the cyst and shunting of an associated hydrocephalus. Syringo-peritoneal shunts were used in 3 children and laminectomy with syringo-subarachnoid shunt in 1 case. The neurological symptoms improved in 57% of the cases, 2 patients deteriorated and 4 patients were lost to follow-up. The authors discuss the clinical symptomatology, the MRI study, the controversies concerning the treatment and concluded with their attitude concerning this pathology in children.
authors.affiliation: Service de Neurochirurgie Pédiatrique, Hôpital des Enfants de La Timone, Marseille.
authors.forename: G
authors.initials: G
authors.lastname: Lena
authors.forename: Z
authors.initials: Z
authors.lastname: Boudawara
authors.forename: L
authors.initials: L
authors.lastname: Genitori
authors.forename: S
authors.initials: S
authors.lastname: Cavalhero
authors.forename: M
authors.initials: M
authors.lastname: Choux
mesh_terms: D000293:Adolescent; D001139:Arnold-Chiari Malformation / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D002557:Cerebrospinal Fluid Shunts; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007796:Laminectomy; D008279:Magnetic Resonance Imaging; D008297:Male; D013595:Syringomyelia / Q000150:complications / Q000175:diagnosis* / Q000601:surgery
vernacular_title: 14 cas de syringomyélie communicante associée à une malformation de Chiari type I chez l'enfant.