[Organization and results of studies on acute hepatic porphyrias in Poland].
The organization, activities and experience of Porphyria Reference Centre of the Institute of Hematology in Poland is shown. A total of 214 families with acute hepatic porphyria were collected. The family studies in search of latent cases were conducted, and measures for preventing the disease attacks were taken. The therapy of the attacks consisted in glucose and heme arginate infusions, and hyperalimentation in the patients is stressed. The incidence rate of porphyrias in Poland, according to the material collected at the Institute of Hematology is 1:15,000 inhabitants, however, it is suggested that the true value is much higher.
Kostrzhevska
E
E
Gregor
A
A
Tarzhinska-Nosal
S
S
D000208:Acute Disease; D005260:Female; D006801:Humans; D015994:Incidence; D008297:Male; D011044:Poland / Q000453:epidemiology; D017094:Porphyrias, Hepatic / Q000453:epidemiology* / Q000517:prevention & control / Q000628:therapy
Organizatsiia i rezul'taty issledovaniia ostrykh pechenochnykh porfiriĭ v Pol'she.