title: [Thrombosis of superior longitudinal sinus and pulmonary embolism in nephrotic syndrome].
abstract: The authors report on the case of a child with the nephrotic syndrome complicated by thrombosis of superior longitudinal sinus, bilateral massive pulmonary embolism resulting in a sudden death. A dramatic deficiency in factor XII was demonstrated; the pathophysiology and management of such an abnormality are discussed.
authors.affiliation: Unité de néphrologie pédiatrique, hôpital E Herriot, Lyon, France.
authors.forename: M C
authors.initials: MC
authors.lastname: Delmas
authors.forename: P
authors.initials: P
authors.lastname: Cochat
authors.forename: B
authors.initials: B
authors.lastname: Ranchin
authors.forename: C
authors.initials: C
authors.lastname: Négrier
authors.forename: P
authors.initials: P
authors.lastname: Barre
authors.forename: R
authors.initials: R
authors.lastname: Bouvier
authors.forename: L
authors.initials: L
authors.lastname: David
mesh_terms: D002675:Child, Preschool; D003520:Cyclophosphamide / Q000627:therapeutic use; D003645:Death, Sudden / Q000209:etiology; D005175:Factor XII Deficiency / Q000209:etiology; D006801:Humans; D008297:Male; D008775:Methylprednisolone / Q000627:therapeutic use; D009404:Nephrotic Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000188:drug therapy; D011655:Pulmonary Embolism / Q000000981:diagnostic imaging / Q000209:etiology*; D011859:Radiography; D012851:Sinus Thrombosis, Intracranial / Q000000981:diagnostic imaging / Q000209:etiology*
chemical_list: D003520:Cyclophosphamide; D008775:Methylprednisolone
vernacular_title: Thrombose du sinus longitudinal supérieur et embolie pulmonaire au cours d'une néphrose.