title: Budd-Chiari syndrome as the primary manifestation of a fibrolamellar hepatocellular carcinoma.
abstract: An 18-year-old female patient was admitted with ascites, right upper abdominal tenderness and peripheral edema. Angiography showed complete occlusion of the vena cava inferior up to the level of the right atrium. By open heart surgery, masses of thrombotic material were pulled out of the v. cava inferior/vv. iliacae which histologically contained tumor cell populations consistent with a hepatocellular carcinoma. Celiacography showed a highly vascularized tumor in the right hepatic lobe. Histologically, it proved to be fibrolamellar subtype hepatocellular carcinoma.
authors.affiliation: Department of Internal Medicine, Georg August University of Göttingen, FRG.
authors.forename: R
authors.initials: R
authors.lastname: Lamberts
authors.forename: R
authors.initials: R
authors.lastname: Nitsche
authors.forename: R E
authors.initials: RE
authors.lastname: de Vivie
authors.forename: W
authors.initials: W
authors.lastname: Peitsch
authors.forename: A
authors.initials: A
authors.lastname: Schauer
authors.forename: R
authors.initials: R
authors.lastname: Schuster
authors.forename: U
authors.initials: U
authors.lastname: Tebbe
authors.forename: H
authors.initials: H
authors.lastname: Kreuzer
authors.forename: W
authors.initials: W
authors.lastname: Creutzfeldt
mesh_terms: D000293:Adolescent; D006502:Budd-Chiari Syndrome / Q000209:etiology* / Q000601:surgery; D006528:Carcinoma, Hepatocellular / Q000150:complications* / Q000235:genetics / Q000601:surgery; D005260:Female; D015972:Gene Expression Regulation, Neoplastic; D016259:Genes, myc / Q000235:genetics; D006801:Humans; D008099:Liver / Q000473:pathology; D008113:Liver Neoplasms / Q000150:complications* / Q000235:genetics / Q000601:surgery