POEMS syndrome: follow-up study of a case.
We report here the case of a 20-year-old man with POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M proteins, skin changes). This rare syndrome followed a 3-year history of a syndrome that mimics a chronic inflammatory demyelinating polyneuropathy (CIDP). Treatment with cyclophosphamide induced regression of the syndrome and improved peripheral nerve conduction.
Crisci
C
C
Fondazione Clinica del Lavoro, Medical Center of Campoli, II School of Medicine, University of Naples, Italy.
Barbieri
F
F
Parente
D
D
Pappone
N
N
Caruso
G
G
D000328:Adult; D001706:Biopsy; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D008854:Microscopy, Electron; D009186:Myelin Sheath / Q000473:pathology; D009413:Nerve Fibers, Myelinated / Q000473:pathology; D009460:Neurologic Examination; D016878:POEMS Syndrome / Q000175:diagnosis* / Q000473:pathology; D013497:Sural Nerve / Q000473:pathology