[Familial complete atrioventricular block in patients with hypertrophic cardiomyopathy].
The association of spontaneous complete heart block and hypertrophic cardiomyopathy is rare. We have studied three patients of the same family, two brothers and one nephew, ages 19-41 years, with hypertrophic cardiomyopathy confirmed by hemodynamic and angiographic studies. All patients were treated with permanent cardiac pacemaker implant. They are asymptomatic, aging 33 to 55 years, with follow-up of 157 to 176 months after the onset of the heart block.
Albanesi Filho
F M
FM
Hospital Universitário Pedro Ernesto, UERJ.
Ginefra
P
P
Castier
M B
MB
da Rocha
P J
PJ
de Albuquerque
D C
DC
D000328:Adult; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications / Q000175:diagnosis / Q000235:genetics* / Q000628:therapy; D005260:Female; D006327:Heart Block / Q000175:diagnosis / Q000209:etiology / Q000235:genetics* / Q000628:therapy; D006801:Humans; D008297:Male; D010138:Pacemaker, Artificial; D010375:Pedigree
Bloqueio atrioventricular total familiar em pacientes com cardiomiopatia hipertrófica.