[The clinical and computed tomographic criteria of the diagnosis of multiple systemic cerebral atrophy with progressive autonomic insufficiency (the Shy-Drager syndrome)].
Based on clinical and CT examination of 3 patients with Shy-Drager syndrome and the reported data, differential diagnosis of the given diseases is under discussion. Shy-Drager syndrome is characterized by CT signs of progressive atrophy of the pons and cerebellum with no essential changes in the supratentorial brain structures. The authors support a proposal to use the term "multiple systemic atrophy" for designation of the disease entity that includes both Shy-Drager syndrome and sporadic patterns of olivopontocerebellar and strionigral degenerations in which the disease debuts by motor disorders of the extrapyramidal and cerebellar nature rather than by vegetative disturbances.
Gubskiĭ
L V
LV
Vavilov
S B
SB
Gurskaia
N Z
NZ
Alimova
E Ia
EIa
D001921:Brain / Q000000981:diagnostic imaging* / Q000473:pathology; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D008875:Middle Aged; D012791:Shy-Drager Syndrome / Q000175:diagnosis* / Q000473:pathology; D014057:Tomography, X-Ray Computed
Klinicheskie i komp'iuterno-tomograficheskie kriterii diagnostiki mnozhestvennoĭ sistemnoĭ atrofii mozga s progrssiruiushcheĭ vegetativnoĭ nedostatochnost'iu (sindroma Shaia--Dreĭdzhera).