title: CT diagnosis of macrodystrophia lipomatosa. A case report.
abstract: Radiographs and CT scans of a 45-year-old male with progressive enlargement of his right upper limb and shoulder are presented. Extensive soft-tissue hypertrophy with linear radiolucent bands (fat) limited to the lateral aspect of the limb were seen. Exostoses-like bony overgrowth were also seen along interphalangeal joints. At CT, hypertrophic adipose tissue intermingling with muscle fibers was demonstrated, a diagnostic finding distinguishing the lesion from plexiform neurofibrolipomatosis, Klippel-Trenaunay syndrome and other angiomatous lesions.
authors.affiliation: Department of Radiodiagnosis, All India Institute of Medical Sciences, New Delhi.
authors.forename: R
authors.initials: R
authors.lastname: Jain
authors.forename: S
authors.initials: S
authors.lastname: Sawhney
authors.forename: M
authors.initials: M
authors.lastname: Berry
mesh_terms: D001132:Arm; D003937:Diagnosis, Differential; D005877:Gigantism / Q000000981:diagnostic imaging*; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000000981:diagnostic imaging; D008068:Lipomatosis / Q000000981:diagnostic imaging*; D008297:Male; D008875:Middle Aged; D017253:Neurofibromatoses / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed