Pheochromocytoma: a frequent indicator for MEN 2.
Pheochromocytoma is a frequent indicator of multiple endocrine neoplasia type 2A (MEN 2A); in the 35 French MEN 2A families in which a pheochromocytoma occurred first in some affected members, 30% of the patients had a pheochromocytoma as the first manifestation constituting 45% of all patients with pheochromocytomas. The finding of a pheochromocytoma is a strong indication for a search for medullary thyroid carcinoma and for initiating family screening.
CHU St. Antoine, Paris, France.
C
C
Calmettes
M
M
Rosenberg-Gourgin
J
J
Caron
N
N
Feingold
D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000235:genetics; D006801:Humans; D009377:Multiple Endocrine Neoplasia / Q000150:complications* / Q000175:diagnosis; D010673:Pheochromocytoma / Q000150:complications* / Q000235:genetics