[Right cardiac insufficiency disclosing systemic mastocytosis].
The authors report the case of a 54-year old woman presenting with right cardiac failure in whom the diagnosis of contemporaneous cutaneous-systemic mast cell disease was made. The cardiac symptoms regressed concomitantly with the vasomotor manifestations of the mast cell disease. Following a review of the principal mast cell mediators, the cardiovascular manifestations of the disease are studied and pathogenetic hypotheses are being put forward.
Morvan
Y
Y
Service de Médecine Interne et Maladies de Système, CHU, Dijon.
Collet
E
E
Bielefeld
P
P
Meyer
P
P
Chantereau
M J
MJ
Baudet
J G
JG
Dalac
S
S
Besancenot
J F
JF
D001707:Biopsy, Needle; D015150:Echocardiography, Doppler; D004804:Eosinophils / Q000502:physiology; D005260:Female; D006632:Histamine / Q000502:physiology; D006801:Humans; D017380:Hypertrophy, Right Ventricular / Q000000981:diagnostic imaging / Q000209:etiology* / Q000503:physiopathology; D008099:Liver / Q000473:pathology; D008415:Mastocytosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology / Q000503:physiopathology; D008875:Middle Aged; D012075:Remission, Spontaneous
D006632:Histamine
Insuffisance cardiaque droite révélatrice d'une mastocytose systémique.