[Right cardiac insufficiency disclosing systemic mastocytosis].
The authors report the case of a 54-year old woman presenting with right cardiac failure in whom the diagnosis of contemporaneous cutaneous-systemic mast cell disease was made. The cardiac symptoms regressed concomitantly with the vasomotor manifestations of the mast cell disease. Following a review of the principal mast cell mediators, the cardiovascular manifestations of the disease are studied and pathogenetic hypotheses are being put forward.
Service de Médecine Interne et Maladies de Système, CHU, Dijon.
Y
Y
Morvan
E
E
Collet
P
P
Bielefeld
P
P
Meyer
M J
MJ
Chantereau
J G
JG
Baudet
S
S
Dalac
J F
JF
Besancenot
D001707:Biopsy, Needle; D015150:Echocardiography, Doppler; D004804:Eosinophils / Q000502:physiology; D005260:Female; D006632:Histamine / Q000502:physiology; D006801:Humans; D017380:Hypertrophy, Right Ventricular / Q000000981:diagnostic imaging / Q000209:etiology* / Q000503:physiopathology; D008099:Liver / Q000473:pathology; D008415:Mastocytosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology / Q000503:physiopathology; D008875:Middle Aged; D012075:Remission, Spontaneous
D006632:Histamine
Insuffisance cardiaque droite révélatrice d'une mastocytose systémique.