Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system.
A 63 year old man with complete atrioventricular block was diagnosed as having Fabry's disease. A short PR interval is a common electrocardiographic finding in Fabry's disease, but complete atrioventricular block is a very rare complication. Necropsy indicated that lipid accumulation in the atrioventricular conduction system was the probable cause of this patient's atrioventricular block.
Ikari
Y
Y
Division of Cardiology, Mitsui Memorial Hospital, Tokyo, Japan.
Kuwako
K
K
Yamaguchi
T
T
D004562:Electrocardiography; D000795:Fabry Disease / Q000473:pathology* / Q000503:physiopathology; D006327:Heart Block / Q000473:pathology* / Q000503:physiopathology; D006329:Heart Conduction System / Q000473:pathology* / Q000503:physiopathology; D006801:Humans; D008297:Male; D008875:Middle Aged