Rare inherited bleeding disorders secondary to coagulation factors in Jordan: a nine-year study.
This work reports on rare inherited coagulation factors defects which were seen in a developing country over a 9-year period. There were a total of 30 cases which fulfilled this diagnosis. Fibrinogen abnormalities were the most frequently encountered. There were 10 patients with afibrinogenemia, 2 with hypofibrinogenemia and 1 case with dysfibrinogenemia. Factor XI deficiency was found in 7 patients, factor V and VII deficiencies accounted for 3 cases each. Factor X and XIII deficiencies were found in 2 patients each. All these rare deficiencies accounted for 10% of all inherited bleeding disorders in the population studied over 9 years.
Awidi
A S
AS
Department of Medicine and Haematology, Faculty of Medicine, Jordan University, Amman.
D001778:Blood Coagulation Disorders / Q000175:diagnosis / Q000453:epidemiology* / Q000235:genetics; D001779:Blood Coagulation Factors / Q000032:analysis*; D001780:Blood Coagulation Tests; D006801:Humans; D007597:Jordan / Q000453:epidemiology; D015995:Prevalence
D001779:Blood Coagulation Factors