[Kasabach-Merritt syndrome. A differential diagnosis in thrombocytopenia].
The Kasabach-Merritt syndrome consists of hemangioma in association with thrombocytopenia and localized consumption coagulopathy. It is primarily a disease of childhood, but may be seen in adult patients too. When untreated, it involves considerable risk of mortality. Two adult patients are described. The disease can be cured by surgery. We discuss different options for treatment when surgery is not feasible.
Tjønnfjord
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GE
Hematologisk seksjon, Rikshospitalet, Oslo.
Evensen
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SA
Slettebø
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H
Sund
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S
D003937:Diagnosis, Differential; D005260:Female; D006392:Hemangioma, Cavernous / Q000097:blood / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008875:Middle Aged; D013160:Splenic Neoplasms / Q000097:blood / Q000175:diagnosis* / Q000473:pathology; D013577:Syndrome; D013921:Thrombocytopenia / Q000175:diagnosis*
Kasabach-Merritts syndrom. En differensialdiagnose ved trombocytopeni.