Recovery from pulmonary hypertension in an adolescent with mixed connective tissue disease.
This paper describes the case of an 11 year old girl who presented with mixed connective tissue disease which was complicated by the development of pulmonary hypertension. This case is unique with respect to the young age of onset, the serial non-invasive method used to follow the disease process, and the favourable response to treatment with vasodilator and anti-inflammatory drugs.
Friedman
D M
DM
Division of Pediatric Cardiology, New York University Medical Center, NY 10016.
Mitnick
H J
HJ
Danilowicz
D
D
D002648:Child; D003520:Cyclophosphamide / Q000627:therapeutic use; D005260:Female; D006801:Humans; D006830:Hydralazine / Q000627:therapeutic use; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology* / Q000503:physiopathology; D008947:Mixed Connective Tissue Disease / Q000150:complications* / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use
D006830:Hydralazine; D003520:Cyclophosphamide; D011241:Prednisone