Laminar heterotopic grey matter (double cortex) in a patient with late onset Lennox-Gastaut syndrome.
The Lennox-Gastaut syndrome (LGS) is a severe epileptic disorder, characterized by developmental delay, typical electroencephalographic pattern and poor control of seizures. This epileptic syndrome generally presents in early childhood but exceptionally starts at the age of 5 years or later. We describe a patient who was classified as late-onset LGS, with evidence of mild hydrocephalus on CT. MRI added new diagnostic information by demonstrating laminar heterotopic grey matter.
Soucek
D
D
Department of Neurology, University of Innsbruck, Austria.
Birbamer
G
G
Luef
G
G
Felber
S
S
Kristmann
E
E
Bauer
G
G
D000328:Adult; D001932:Brain Neoplasms / Q000150:complications* / Q000175:diagnosis; D002540:Cerebral Cortex; D002828:Choristoma / Q000150:complications* / Q000175:diagnosis; D004569:Electroencephalography; D004832:Epilepsy, Absence / Q000209:etiology*; D004829:Epilepsy, Generalized / Q000209:etiology*; D004830:Epilepsy, Tonic-Clonic / Q000209:etiology*; D005260:Female; D006801:Humans; D008607:Intellectual Disability / Q000209:etiology; D008279:Magnetic Resonance Imaging; D014057:Tomography, X-Ray Computed