title: [Abnormalities in the signal-averaged electrocardiogram in Ebstein's anomaly].
abstract: Abnormalities in the signal-averaged electrocardiogram (SAECG) of patients with Ebstein's anomaly were studied. A SAECG was obtained in 4 patients with Ebstein's anomaly, aged 3 to 25 years. The control groups included 8 patients with atrial septal defect (ASD group), 10 with right bundle branch block (RBBB group), 8 with Wolff-Parkinson-White (WPW) syndrome (WPW group), and 40 normal subjects (Normal group). The SAECG was calculated by the vector-magnitude method using the VCM-3000. The root-mean-square during the initial 20 msec of the filtered QRS (i-RMS) was very small in 2 older patients with Ebstein's anomaly compared to the ASD group, the RBBB group and the Normal group, and was as small as that in the WPW group. This probably was affected by the delta wave associated with Ebstein's anomaly or concealed accessory pathway. The root-mean-square during the terminal 40 msec of the filtered QRS (t-RMS) was small in the patients with Ebstein's anomaly and the RBBB group. Two patients with Ebstein's anomaly had a smaller t-RMS than the RBBB group, suggesting pathological changes of an atrialized right ventricle. In conclusion, SAECG is useful for evaluating patients with Ebstein's anomaly, especially older patients.
authors.affiliation: Department of Pediatrics, University of Tokushima, School of Medicine.
authors.forename: H
authors.initials: H
authors.lastname: Akita
authors.forename: S
authors.initials: S
authors.lastname: Matsuoka
authors.forename: Y
authors.initials: Y
authors.lastname: Taguchi
authors.forename: M
authors.initials: M
authors.lastname: Kubo
authors.forename: Y
authors.initials: Y
authors.lastname: Hayabuchi
authors.forename: Y
authors.initials: Y
authors.lastname: Kuroda
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D002675:Child, Preschool; D004437:Ebstein Anomaly / Q000175:diagnosis* / Q000473:pathology; D004562:Electrocardiography / Q000379:methods*; D005260:Female; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D008297:Male