title: [Pulmonary valve atresia with ventricular septum defect: interventional recanalization of the right ventricular outflow tract].
abstract: A case of pulmonary atresia with ventricular septal defect is reported where continuity between the right ventricle and the hypoplastic pulmonary artery was established interventionally. The atretic valve was perforated using a special "perforation needle" with a sharp and stiff distal and a flexible proximal part. Perforation of the bifurcation was well tolerated without later sequelae. After perforation of the atresia, dilation was successfully performed using 2, 4, and 7.2 mm balloons with a pressure of 10 atm; the arterial oxygen saturation increased from 72% to 84%. Four weeks later repeated "valvuloplasty" was performed (balloon diameters 8 mm, 9.5 mm, and 12 mm) and the "valve" ring was dilated to a diameter of 10.5 mm. Although no general conclusions can be drawn from this single application, mechanical perforation of the atresia could become an attractive interventional approach for the treatment of pulmonary atresia.
authors.affiliation: Abteilung Angeborene Herzfehler/Kinderkardiologie, Deutsches Herzzentrum Berlin.
authors.forename: G
authors.initials: G
authors.lastname: Hausdorf
authors.forename: M
authors.initials: M
authors.lastname: Schneider
authors.forename: I
authors.initials: I
authors.lastname: Schulze-Neick
authors.forename: P E
authors.initials: PE
authors.lastname: Lange
mesh_terms: D000792:Angiography; D002648:Child; D003097:Collateral Circulation / Q000502:physiology; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D011183:Postoperative Complications / Q000000981:diagnostic imaging; D011651:Pulmonary Artery / Q000002:abnormalities*; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000601:surgery*
vernacular_title: Pulmonalklappenatresie mit Ventrikelseptumdefekt: Interventionelle Rekanalisation des rechtsventrikulären Ausflusstraktes.