title: [McCune-Albright syndrome in association with meningioma and mental and psychological retardation].
abstract: Report of a boy aged 17 years and review of the literature on the neoplasias of CAS. The cause of examination was a psychic maldevelopment. Cranial arteriography exhibited extreme wide Carotis communis and CT temporal meningioma right and septum pellucidum cyste. A psychic frontal lobe syndrome and cosmetic impairment by skull changes of the CAS are discussed being partial causes of the psychic maldevelopment. Atypical there were retardation of calcification and dentition, bilateral coarctation of the auditory passage with resulting hearing loss. Till now only J. Frankel and coworkers have published the case of a 50 year old Pakistani with the combination of CAS and Meningioma as a complication of fibrous dysplasia of the skull. We suppose relations between CAS and neurofibromatosis and its blastomatous tendency to meningioma.
authors: Landesfachkrankenhaus für Psychiatrie und Neurologie, Mühlhausen/Thür.
authors: P
authors: P
authors: Fehlow
authors: F
authors: F
authors: Walther
authors: H
authors: H
authors: Assmann
mesh_terms: D000293:Adolescent; D001289:Attention Deficit Disorder with Hyperactivity / Q000000981:diagnostic imaging* / Q000523:psychology; D005359:Fibrous Dysplasia, Polyostotic / Q000000981:diagnostic imaging* / Q000523:psychology; D005624:Frontal Bone / Q000000981:diagnostic imaging; D006801:Humans; D008607:Intellectual Disability / Q000000981:diagnostic imaging* / Q000523:psychology; D008297:Male; D008577:Meningeal Neoplasms / Q000000981:diagnostic imaging* / Q000523:psychology; D008579:Meningioma / Q000000981:diagnostic imaging* / Q000523:psychology; D019965:Neurocognitive Disorders / Q000000981:diagnostic imaging* / Q000523:psychology; D010553:Personality Development; D013701:Temporal Bone / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed
vernacular_title: McCune-Albright-Syndrom in Assoziation mit Meningeom sowie mentaler und psychischer Retardierung.