Polysplenia syndrome with various visceral anomalies in an adult: embryological and clinical considerations.
A 26-year-old female with polysplenia syndrome is reported. She had numerous visceral anomalies including polysplenia, a short pancreas, a preduodenal portal vein, malrotation of the bowel, azygos continuation of the inferior vena cava, bilateral hyparterial bronchi and symmetrical liver lobation. Embryological and clinical considerations of polysplenia syndrome are described.
Muneta
S
S
Department of Internal Medicine, Matsuyama Red Cross Hospital, Ehime, Japan.
Sakai
S
S
Fukuda
H
H
Imamura
Y
Y
Matsumoto
I
I
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000328:Adult; D001401:Azygos Vein / Q000002:abnormalities; D005260:Female; D006801:Humans; D008099:Liver / Q000002:abnormalities*; D008279:Magnetic Resonance Imaging; D010179:Pancreas / Q000002:abnormalities*; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography; D014682:Vena Cava, Inferior / Q000002:abnormalities*