Cochlear implants for congenital deformities.
There have been few accounts of multi-channel cochlear implants in patients with congenital structural deformities of the inner ear which are associated with severe and sometimes progressive deafness. These malformations can now be recognized easily on 2 plane thin section high resolution CT studies which are mandatory for the pre-implantation assessment. However, no attempt seems to have been made to describe which of these malformations would be suitable for an implant or for which would this procedure be contra-indicated. True Mondini deformity of both the cochlea and dilated vestibular aqueduct type would appear suitable for a multi channel implant, but this type of implant should not be used for a primitive otocyst, severe labyrinthine dysplasia or the characteristic X-linked deformity.
Phelps
P D
PD
Royal National Throat, Nose and Ear Hospital, London.
D003051:Cochlea / Q000002:abnormalities; D003052:Cochlear Aqueduct / Q000002:abnormalities; D003054:Cochlear Implants; D003638:Deafness / Q000000981:diagnostic imaging / Q000235:genetics / Q000601:surgery*; D007758:Ear, Inner / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed; D014960:X Chromosome