An unusual case of choledochal cyst causing hepatic failure requiring orthotopic liver transplantation.
The authors describe a case of orthotopic liver transplantation (OLT) in a patient with an infantile form of choledochal cyst that progressed to severe hepatic failure. Choledochal cyst must be included in the differential diagnosis of extrahepatic biliary obstruction in infants; it represents an additional reason to consider early exploratory laparotomy, both for diagnosis and to perform definitive excision. In the event that end-stage liver disease develops, OLT should be considered.
Castaldo
P
P
Department of Surgery, University of Nebraska Medical Center, Omaha 68198-3208.
Grazi
G L
GL
Wood
R P
RP
Markin
R S
RS
Stratta
R J
RJ
Langnas
A N
AN
Clark
J H
JH
Shaw
B W
BW
D015529:Choledochal Cyst / Q000150:complications* / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007223:Infant; D008105:Liver Cirrhosis, Biliary / Q000209:etiology; D017093:Liver Failure / Q000209:etiology* / Q000601:surgery; D016031:Liver Transplantation