Intercurrent illness in inborn errors of intermediary metabolism.
Metabolic decompensation may occur in patients with disorders of intermediary metabolism during intercurrent illness. To prevent complications it is normal practice to change the diet to an 'emergency regimen'. The mainstay of this is a high carbohydrate intake, using soluble glucose polymer, given as frequent drinks by day and during the night. Additional therapy is given for some disorders. Practical details of the treatment are outlined.
Dixon
M A
MA
Hospital for Sick Children, London.
Leonard
J V
JV
D000138:Acidosis / Q000378:metabolism; D002648:Child; D002675:Child, Preschool; D004630:Emergencies; D005227:Fatty Acids / Q000378:metabolism; D006266:Health Education; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008375:Maple Syrup Urine Disease / Q000178:diet therapy / Q000378:metabolism; D008661:Metabolism, Inborn Errors / Q000178:diet therapy* / Q000378:metabolism; D010290:Parents; D011506:Proteins / Q000378:metabolism; D014508:Urea / Q000378:metabolism
D005227:Fatty Acids; D011506:Proteins; D014508:Urea