[Disseminated complex vascular malformations].
Diffuse complex vascular malformations are sporadic or hereditary. They usually concern one type of vessel: capillary, venous or arterial (with AV fistula). They involve skin, mucosal membranes and internal organs. They lead to a rich and heterogeneous symptomatology, depending on the lesional localizations. Five out of them are described: cutis marmorata, Rendu Osler disease, Bean syndrome, Maffucci syndrome, and Proteus syndrome.
Enjolras
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Service du Pr. Merland, hôpital Lariboisière, Paris.
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D001165:Arteriovenous Malformations / Q000175:diagnosis*; D004687:Enchondromatosis / Q000175:diagnosis; D006801:Humans; D009506:Nevus / Q000175:diagnosis; D016715:Proteus Syndrome / Q000175:diagnosis; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000175:diagnosis; D013684:Telangiectasis / Q000175:diagnosis
Malformations vasculaires complexes disséminées.