[Supravalvular aortic stenosis and coronary aneurysm].
A 32-year old woman, with endocarditis caused by Streptococcus mitis, and systolic murmur is presented. The Doppler examination was found a systolic gradient of 150 mmHg. Aortography showed a multiple membranous supravalvular aortic stenosis, with aneurysmal dilatation of the left main coronary artery and circumflex artery, associated with bicuspid aortic valve and mild aortic insufficiency. The patient died suddenly by cardiac arrest in stand by to cardiac surgery. Anatomic comprobation was not possible. The coronary artery anomalies associated with the supravalvular aortic stenosis syndrome are reviewed.
Martínez Sande
J L
JL
Sección de Cardiología, Complexo Hospitalario Cristal-Piñor, Orense.
Amaro Cendón
A
A
Blanco Labrador
E
E
Pérez Rodríguez
M
M
Sánchez Prieto
A
A
Iglesias Carreño
C
C
Gil de la Peña
M
M
D000328:Adult; D001024:Aortic Valve Stenosis / Q000150:complications*; D003323:Coronary Aneurysm / Q000150:complications*; D005260:Female; D006801:Humans
Estenosis aórtica supravalvular y aneurisma coronario.