Pulmonary alveolar microlithiasis and lymphocytic interstitial pneumonitis in a ten year old girl.
Pulmonary alveolar microlithiasis (PAM) is a rare lung disease, characterized by progressive formation of intra-alveolar calculi in response to an unknown stimulus. We report an unusual presentation of PAM in a 10 year old girl with clinically significant interstitial lung disease and histological evidence of both PAM and lymphocytic interstitial pneumonitis. A rapid improvement of pulmonary function and exercise tolerance was seen in response to glucosteroid therapy.
Ratjen
F A
FA
Pulmonary Dept., Children's Hospital of Essen, Germany.
Schoenfeld
B
B
Wiesemann
H G
HG
D001992:Bronchoalveolar Lavage Fluid / Q000166:cytology; D002137:Calculi / Q000150:complications* / Q000473:pathology; D002648:Child; D005260:Female; D006801:Humans; D007958:Leukocyte Count; D008171:Lung Diseases / Q000150:complications / Q000473:pathology; D008214:Lymphocytes; D011241:Prednisone / Q000627:therapeutic use; D011650:Pulmonary Alveoli / Q000473:pathology*; D011658:Pulmonary Fibrosis / Q000150:complications* / Q000188:drug therapy / Q000473:pathology
D011241:Prednisone