Fatal pulmonary arterial hypertension complicating noncirrhotic portal fibrosis.
A 25-yr-old female with noncirrhotic portal fibrosis underwent a lienorenal shunt for variceal bleed. Ten years after shunt surgery, she presented with progressive breathlessness, and severe pulmonary arterial hypertension was detected, to which she subsequently succumbed. Autopsy revealed classical plexogenic pulmonary arteriopathy.
Goenka
M K
MK
Department of Gastroenterology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
Mehta
S K
SK
Malik
A K
AK
Kumar
Y R
YR
Kochhar
R
R
D000328:Adult; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications*; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008103:Liver Cirrhosis / Q000150:complications*