title: Bannayan-Zonana syndrome associated with lipomas, hemangiomas, and lymphangiomas.
abstract: Bannayan-Zonana syndrome is a rare disorder characterized by macrocephaly and multiple soft tissue and visceral hamartomas. This report presents a sporadic patient with macrocephaly, lipomas, hemangiomas, and lymphangiomas who died of cardiac and respiratory failure due to progressive cervicomediastinal arteriovenous fistulous hemangiomas at the age of 9 years.
authors.affiliation: Department of Pediatric Surgery, Tohoku University School of Medicine, Sendai, Japan.
authors.forename: Y
authors.initials: Y
authors.lastname: Hayashi
authors.forename: R
authors.initials: R
authors.lastname: Ohi
authors.forename: Y
authors.initials: Y
authors.lastname: Tomita
authors.forename: T
authors.initials: T
authors.lastname: Chiba
authors.forename: Y
authors.initials: Y
authors.lastname: Matsumoto
authors.forename: T
authors.initials: T
authors.lastname: Chiba
mesh_terms: D000015:Abnormalities, Multiple; D001164:Arteriovenous Fistula; D005260:Female; D006222:Hamartoma; D006257:Head / Q000002:abnormalities*; D006391:Hemangioma; D006801:Humans; D007223:Infant; D008067:Lipoma; D008202:Lymphangioma; D009378:Neoplasms, Multiple Primary; D011379:Prognosis; D012983:Soft Tissue Neoplasms; D013577:Syndrome