Dislocation of the crystalline lens in a patient with Sturge-Weber syndrome.
A moderately retarded institutionalized patient diagnosed with Sturge-Weber syndrome and bilateral retinitis pigmentosa underwent enucleation OD because of intractable pain secondary to glaucoma in 1965. Twenty-three years later, the patient had a dislocated lens OS. Although the lens dislocation might have been caused by trauma, it also might be associated with either Sturge-Weber syndrome or retinitis pigmentosa. The role of protective eye wear in one-eyed institutionalized retarded patients is discussed. To our knowledge, this combination of Sturge-Weber syndrome, bilateral retinitis pigmentosa, and a dislocated lens has not been reported previously.
Filatov
V
V
Wilmer Ophthalmological Institute, Johns Hopkins Hospital, Baltimore, Maryland.
Guyer
D R
DR
Lustbader
J M
JM
Berkow
J W
JW
D002386:Cataract / Q000150:complications; D002387:Cataract Extraction; D006801:Humans; D008607:Intellectual Disability / Q000150:complications; D007906:Lens Subluxation / Q000150:complications*; D008297:Male; D008875:Middle Aged; D012174:Retinitis Pigmentosa / Q000150:complications; D013341:Sturge-Weber Syndrome / Q000150:complications*; D014821:Vitrectomy