[The orodental findings in the Ehlers-Danlos syndrome. A report of 2 clinical cases].
Ehlers-Danlos syndrome (EDs) is a hereditary disorder of the connective tissue. Its clinical expression is variable and there are many difficulties in recognizing the disease because of the presence of eleven different forms. In this study the authors describe the oral manifestations in two cases of EDs. The children show hyperelasticity of the skin, easy bruisability, hyperextensibility of the joints, several dental manifestations: periodontitis, many caries, supernumerary teeth or hypodontia.
Majorana
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A
Clinica Odontoiatrica, Università di Brescia.
Facchetti
F
F
D001706:Biopsy; D002648:Child; D004535:Ehlers-Danlos Syndrome / Q000145:classification / Q000175:diagnosis* / Q000473:pathology; D005260:Female; D005881:Gingiva / Q000473:pathology; D006801:Humans; D008297:Male; D009059:Mouth Diseases / Q000145:classification / Q000175:diagnosis* / Q000473:pathology; D014070:Tooth / Q000473:pathology; D014076:Tooth Diseases / Q000145:classification / Q000175:diagnosis* / Q000473:pathology
Rilievi odontostomatologici nella sindrome di Ehler-Danlos. Presentazione di 2 casi clinici.