Patent ductus venosus with hypoplastic right hepatoportal system in a young child born with asymmetric intra-uterine growth retardation.
We report a functioning ductus venosus with hypoplasia of the right hepatoportal system in a 2-year-old child born with asymmetric intra-uterine growth retardation. Postprandial galactosaemia and hyperammonaemia were clues to diagnosis of portal-systemic shunt through the patent ductus venosus, which was confirmed by ultrasonography and angiography.
Maisawa
S
S
Department of Paediatrics, Morioka Children's Hospital, Japan.
Takasago
Y
Y
Oyake
Y
Y
Maeta
H
H
Fujiwara
T
T
D000015:Abnormalities, Multiple; D000641:Ammonia / Q000097:blood; D015901:Angiography, Digital Subtraction; D002675:Child, Preschool; D005317:Fetal Growth Retardation / Q000150:complications*; D005693:Galactosemias / Q000209:etiology; D006801:Humans; D008297:Male; D011168:Portal System / Q000002:abnormalities* / Q000000981:diagnostic imaging; D014463:Ultrasonography; D014471:Umbilical Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging
D000641:Ammonia