Erythrodermic mastocytosis.
Erythrodermic mastocytosis is a rare variant of diffuse cutaneous mastocytosis in which the skin becomes red, thickened, and lichenified and has a doughy consistency with multiple small papules on its surface, giving a leathery appearance to the skin. In this report, I describe a curious case of erythrodermic mastocytosis that appears to be due to vasodilation rather than to mast cell infiltration of the skin. In my opinion, this case might be an example of generalized telangiectasia macularis eruptiva perstans. Results of all laboratory tests failed to demonstrate systemic mast cell involvement; therapy with a combination of H1 and H2 antihistamines plus disodium cromoglycate controlled the symptoms.
Requena
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Servicio de Dermatología, Hospital Militar, Valencia, Spain.
D000328:Adult; D001706:Biopsy; D003873:Dermatitis, Exfoliative / Q000188:drug therapy / Q000209:etiology / Q000473:pathology*; D006801:Humans; D008297:Male; D012867:Skin / Q000473:pathology*; D014582:Urticaria Pigmentosa / Q000150:complications / Q000188:drug therapy / Q000473:pathology*