Anaesthetic problems in a child with ectrodactyly, ectodermal dysplasia and cleft lip/palate. The EEC syndrome.
The EEC syndrome is a congenital anomaly complex associated with ectrodactyly, ectodermal dysplasia, and cleft lip and palate. We present a patient with the complete form of this syndrome who had undergone eight operations in childhood. The main problems encountered by the anaesthetists were malnutrition, difficulty with control of body temperature related to hypohidrosis and persistent infection of the respiratory tract.
Mizushima
A
A
Department of Anesthesiology, Juntendo University School of Medicine, Tokyo, Japan.
Satoyoshi
M
M
D000015:Abnormalities, Multiple / Q000601:surgery*; D000758:Anesthesia / Q000379:methods*; D002675:Child, Preschool; D002971:Cleft Lip / Q000601:surgery*; D002972:Cleft Palate / Q000601:surgery*; D004476:Ectodermal Dysplasia / Q000601:surgery; D005260:Female; D005532:Foot Deformities, Congenital / Q000601:surgery*; D006228:Hand Deformities, Congenital / Q000601:surgery*; D006801:Humans; D007223:Infant; D012086:Reoperation