Severe pulmonary stenosis and interruption of the aortic arch.
A case of severe pulmonary stenosis associated with a subpulmonary ventricular septal defect and interruption of the aortic arch is described in a 5-month-old girl. This combination defies explanation by current theories of the development of obstructive abnormalities of the aortic arch secondary to reduced aortic flow during fetal life, and, to the best of our knowledge, is the first reported case with this particular association.
Blackburn
M E
ME
Department of Paediatric Cardiology, Killingbeck Hospital, Leeds, West Yorkshire, U.K.
Gibbs
J L
JL
Sethia
B
B
D000792:Angiography; D001013:Aorta, Thoracic / Q000002:abnormalities*; D006328:Cardiac Catheterization; D004452:Echocardiography; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000175:diagnosis* / Q000196:embryology; D006801:Humans; D007231:Infant, Newborn; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000175:diagnosis* / Q000196:embryology