Preserved para-arteriolar retinal pigment epithelium retinitis pigmentosa.
In two patients, we studied retinitis pigmentosa with preservation of the retinal pigment epithelium adjacent to and under the retinal arterioles (despite panretinal degeneration). Both patients with preserved para-arteriolar retinal pigment epithelium also exhibited a peculiarly strong hyperopia. In addition to previously reported features, these patients also had sheathing of the major vascular arcades, which suggested a vascular involvement in this uncommon form of retinitis pigmentosa.
Porta
A
A
San Paolo Hospital, Department of Ophthalmology, University of Milan, Italy.
Pierrottet
C
C
Aschero
M
M
Orzalesi
N
N
D000328:Adult; D001160:Arterioles / Q000473:pathology; D002648:Child; D005260:Female; D005451:Fluorescein Angiography; D005654:Fundus Oculi; D006801:Humans; D006956:Hyperopia / Q000473:pathology; D010857:Pigment Epithelium of Eye / Q000473:pathology*; D012171:Retinal Vessels / Q000473:pathology*; D012174:Retinitis Pigmentosa / Q000473:pathology*; D014792:Visual Acuity