[The complete testicular feminization syndrome: apropos 2 new cases].
Two additional cases of complete testicular feminization syndrome or Morris syndrome are described. The patients had consulted for primary amenorrhea. Patient work up revealed a female phenotype, hormone profile and 46,XY karyotype. They were submitted to abdominal surgical exploration and orchidectomy of the cryptorchid male gonads. The potential etiologic factors, pathogenesis, incidence and clinical features of this syndrome are discussed. Furthermore, the surgical treatment and outcome are described, highlighting the incidence of gonadal malignancy if these are not removed early.
Belvís Esclapés
V
V
Servicio de Urología, Hospital del SVS, Alicante, España.
Fernández García
J
J
Lobato Encinas
J
J
Gassó Matoses
M
M
Sánchez Marcos
M
M
Merenciano Cortina
F
F
Mira Llinares
A
A
D000328:Adult; D013734:Androgen-Insensitivity Syndrome / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D009919:Orchiectomy; D013737:Testis / Q000473:pathology
Síndrome de feminización testicular completo: a propósito de dos nuevos casos.