[Sclerosing intravascular bronchiolo-alveolar tumor].
We report the case of a 56 year old female who was admitted to hospital in 1980 for assessment of disseminated nodular pulmonary opacities. The histological examination of a prescalene node biopsy showed features which were compatible with sarcoidosis. No treatment was given. In 1987 a discrete increase in the pulmonary nodules was noted. In 1989 effort dyspnoea occurred and there were pains in the right lower chest and an evening fever. The chest X-ray showed a right sided pleurisy and an increase in the size of the nodules with mediastinal lymphadenopathy. A histological examination of a pulmonary nodule, which was taken at an open lung biopsy enabled the diagnosis of a broncho-alveolar sclerosing intravascular tumour to be established. This is a rare tumour which has a slow evolution occurring most often in middle aged females. In 50% of cases the discovery is fortuitous. Besides patients present with non-specific symptoms. The radiological examination reveals multiple nodular opacities which are diffuse and 0.5 to 1.5 cm in diameter. Currently these tumours do not benefit from any particular therapy.
Schwartz
A
A
Service de Pneumologie, Centre Hospitalier Universitaire, Tours.
De Muret
A
A
Lemaire
B
B
Patte
F
F
Lemarié
E
E
D003937:Diagnosis, Differential; D005260:Female; D006390:Hemangioendothelioma / Q000473:pathology*; D006801:Humans; D008171:Lung Diseases / Q000175:diagnosis; D008175:Lung Neoplasms / Q000473:pathology*; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D012507:Sarcoidosis / Q000175:diagnosis; D012598:Sclerosis
Tumeur sclérosante intravasculaire bronchiolo-alvéolaire.