Spastic paraparesis associated with portal-systemic venous shunting due to congenital hepatic fibrosis.
We report a case of progressive spastic paraparesis in a 45-year-old man with total portal-systemic shunting, which developed spontaneously due to congenital hepatic fibrosis. Cellular functions of the liver, except for an elevated blood ammonia level, were within normal limits, as is usual in congenital hepatic fibrosis. This case shows that spastic paraparesis following portal-systemic shunting may occur without liver failure.
Demirci
M
M
Department of Neurology, Faculty of Medicine, Hacettepe University, Ankara, Turkey.
Tan
E
E
Elibol
B
B
Gedikoğlu
G
G
Saribaş
O
O
D000641:Ammonia / Q000097:blood; D006801:Humans; D008102:Liver Circulation; D008103:Liver Cirrhosis / Q000150:complications* / Q000151:congenital; D008297:Male; D008875:Middle Aged; D009128:Muscle Spasticity / Q000209:etiology / Q000503:physiopathology; D010264:Paraplegia / Q000209:etiology* / Q000503:physiopathology; D011168:Portal System / Q000503:physiopathology
D000641:Ammonia