title: Pulmonary lymphangiomyomatosis treated by single lung transplantation.
abstract: Pulmonary lymphangiomyomatosis is a rare disease resistant to almost all medical treatments to date. We describe the case of a 44-yr-old woman with end-stage pulmonary lymphangiomyomatosis who was treated by single-lung transplantation. The patient is doing well in her sixteenth post-transplantation month and has a marked improvement in her pulmonary function tests and walking distance as compared with preoperative values, and she is enjoying an unrestricted life-style.
authors.affiliation: Service de Pneumologie et Réanimation, Hôpital Beaujon, Clichy, France.
authors.forename: C
authors.initials: C
authors.lastname: Sleiman
authors.forename: H
authors.initials: H
authors.lastname: Mal
authors.forename: G
authors.initials: G
authors.lastname: Jebrak
authors.forename: C
authors.initials: C
authors.lastname: Darne
authors.forename: E
authors.initials: E
authors.lastname: Meeus
authors.forename: F
authors.initials: F
authors.lastname: Dubois
authors.forename: M
authors.initials: M
authors.lastname: Luisetti
authors.forename: M
authors.initials: M
authors.lastname: Fournier
authors.forename: R
authors.initials: R
authors.lastname: Pariente
authors.forename: B
authors.initials: B
authors.lastname: Andreassian
mesh_terms: D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000453:epidemiology / Q000601:surgery*; D016040:Lung Transplantation; D008203:Lymphangiomyoma / Q000453:epidemiology / Q000601:surgery*; D011859:Radiography; D011877:Radionuclide Imaging; D012129:Respiratory Function Tests