[Kidney carcinoma in Bourneville-Pringle disease].
We report a case of renal cell carcinoma in a 28-year-old woman with Bourneville-Pringle's disease. A review of the literature revealed 16 cases of renal cell carcinoma associated with tuberous sclerosis. The incidence of angiomyolipoma among patients with Bourneville-Pringle's disease is cited in the literature as 40-80%, but this is based solely on two early publications, while other publications suggest a considerably higher incidence of renal cell carcinoma in Bourneville-Pringle's disease, as in other phacomatoses (Hippel-Lindau's disease). We therefore recommend screening for renal cell carcinoma in patients with Bourneville-Pringle's disease.
Gottfried
H W
HW
Urologische Universitätsklinik Ulm.
Miller
K
K
de Petriconi
R
R
Wenderoth
U K
UK
Hautmann
R E
RE
D000328:Adult; D002277:Carcinoma / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D007668:Kidney / Q000473:pathology; D007680:Kidney Neoplasms / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D008207:Lymphatic Metastasis; D009392:Nephrectomy; D014402:Tuberous Sclerosis / Q000150:complications* / Q000473:pathology / Q000601:surgery
Nierenkarzinom beim Morbus Bourneville-Pringle.