Pulmonary lymphangiomyomatosis treated by single lung transplantation.
Pulmonary lymphangiomyomatosis is a rare disease resistant to almost all medical treatments to date. We describe the case of a 44-yr-old woman with end-stage pulmonary lymphangiomyomatosis who was treated by single-lung transplantation. The patient is doing well in her sixteenth post-transplantation month and has a marked improvement in her pulmonary function tests and walking distance as compared with preoperative values, and she is enjoying an unrestricted life-style.
Sleiman
C
C
Service de Pneumologie et Réanimation, Hôpital Beaujon, Clichy, France.
Mal
H
H
Jebrak
G
G
Darne
C
C
Meeus
E
E
Dubois
F
F
Luisetti
M
M
Fournier
M
M
Pariente
R
R
Andreassian
B
B
D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000453:epidemiology / Q000601:surgery*; D016040:Lung Transplantation; D008203:Lymphangiomyoma / Q000453:epidemiology / Q000601:surgery*; D011859:Radiography; D011877:Radionuclide Imaging; D012129:Respiratory Function Tests