[Idiopathic external hydrocephaly and familial macrocephaly in infancy].
Idiopathic external hydrocephalus is a frequent cause of macrocephaly in infants. The cranial CT scan shows an enlarged subarachnoid space, especially in the frontal area, with a prominent interhemispheric fissure and occasionally an enlargement of the ventricular system. Sixteen patients with this condition are reported; 7 of which had a family history of megalo-encephaly and 4 had delayed motor development, although it was transient in 3 of the cases. The cranial circumference was normal at about 18 months of age, but 4 patients had megalo-encephaly after 3 years of age. The radiological images were normal in all cases between 24 and 48 months of age without treatment.
Palencia Luaces
R
R
Neuropediatría, Hospital Universitario, Facultad de Medicina, Valladolid.
Aldana Gómez
J
J
Tresierra Unzaga
F
F
D000015:Abnormalities, Multiple / Q000235:genetics; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000000981:diagnostic imaging* / Q000235:genetics; D007223:Infant; D008297:Male; D012886:Skull / Q000002:abnormalities* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed
Hidrocefalia externa idiopática en la infancia y macrocefalia familiar.