[Prune Belly syndrome. A case of recurrence].
Prune belly syndrome is rare. It involves a combination of muscular hypoplasia of the abdominal wall, marked dilatation of the bladder and ureters and, in its most severe form, bilateral testicular ectopia. Fetuses of both sexes may be affected, with a marked predominance of males. The prognosis is poor, with a mortality rate in excess of 50%, due essentially to renal and respiratory complications. The authors evaluate the prognosis of Prune Belly syndrome with regard to a case of recurrence and suggest a modern approach to its management.
Darmon
J C
JC
Service de Gynécologie-Obstétrique, CHRU, Pointe-à-Pitre.
Janky
E
E
Couchy
B
B
D000032:Abortion, Therapeutic; D000328:Adult; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D011379:Prognosis; D011535:Prune Belly Syndrome / Q000000981:diagnostic imaging* / Q000401:mortality / Q000473:pathology; D012008:Recurrence; D016216:Ultrasonography, Prenatal
Syndrome de Prune Belly. A propos d'un cas de récurrence.