[Anomalous origin of the right pulmonary artery from the ascending aorta. Its surgical correction in early infancy].
Anomalous origin of the right pulmonary artery from the ascending aorta is a rare congenital malformation associated with a high mortality during the first year of life. Up to 1990, 75 cases have been reported in the literature. We are reporting 2 cases diagnosed and operated before 3 months of age. Repair was facilitated by the use of deep hypothermic circulatory arrest. The duration of follow up is 5 and 6 years, respectively. Pre and postoperative cardiac catheterization pressure data and angiograms are shown. We review the literature, presenting the physiopathological, embryological and surgical features of this rare congenital anomaly.
Caffarena Calvar
J M
JM
Servicio de Cirugía Cardiovascular, Hospital Infantil La Fe, Valencia.
Gómez Ullate
J M
JM
Caffarena Raggio
J M
JM
Sáez Palacios
J M
JM
Malo Concepción
P
P
D001011:Aorta / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D001027:Aortography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery
Origen anómalo de la arteria pulmonar derecha de la aorta ascendente. Corrección quirúrgica en la primera infancia.