[The reactive hemophagocytic syndrome associated with immunoblastic B-cell lymphoma].
The reactive hemophagocytic syndrome is a rare clinical-pathological entity which usually has a benign evolution and which is characterized by the systemic proliferation of mature histiocytes, with a great phagocytosis ability and which occurs in a secondary form in some infections and neoplasias and after the administration of certain drugs. We present a case of reactive hemophagocytic syndrome in a patient presenting a non-Hodgkin lymphoma, of crest malignancy, B immunoblastic and kappa monoclonal, with fatal evolution and in which the diagnosis was obtained after necropsy.
Barberán
J
J
Servicio de Enfermedades Infecciosas, H.M.C. Gómez Ulla, Madrid.
Pastor
J M
JM
Menéndez
M A
MA
Ortiz
S
S
de la Cruz
A
A
Sánchez
T
T
D000368:Aged; D015616:Histiocytosis, Non-Langerhans-Cell / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D007145:Immunoglobulin kappa-Chains / Q000032:analysis; D007150:Immunohistochemistry; D008198:Lymph Nodes / Q000473:pathology; D016400:Lymphoma, Large-Cell, Immunoblastic / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D013154:Spleen / Q000473:pathology
D007145:Immunoglobulin kappa-Chains
Síndrome hemofagocítico reactivo asociado a linfoma inmunoblástico B.