[Pathogenesis of juvenile muscular atrophy of unilateral upper extremity in reference to venous congestion of epidural space].
MRI and dynamic CT studies were performed in a young male with juvenile muscular atrophy of unilateral upper extremity (JM) with onset at age 15 and clinical course of 2 years. The mechanism of development of congestion in vertebral venous plexus was considered. Dynamic CT of the head in the neck flexion showed rapid reflux of blood from the intervertebral veins into the posterior internal vertebral venous plexus at the C5-C6 level and consequent congestion. It is speculated that in this patient some mechanism associated with head anteflexion led to a reflux into the valveless posterior internal vertebral venous plexus and congestion as well. Furthermore, it could be considered that anterior shift of the dural sac at the time of head anteflexion plays an important role in the development of this internal vertebral venous plexus congestion in JM.
Murata
K
K
Department of Neurology, Nara Medical University.
Iwasaki
S
S
Mano
Y
Y
Nakagawa
H
H
Takayanagi
T
T
D000293:Adolescent; D001132:Arm; D004824:Epidural Space / Q000098:blood supply; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009133:Muscular Atrophy / Q000175:diagnosis / Q000209:etiology*; D014057:Tomography, X-Ray Computed; D014689:Venous Insufficiency / Q000150:complications*