Late onset familial Hallervorden-Spatz disease: MR findings in two sisters.
Two sisters affected by late onset Hallervorden-Spatz disease are described. In both patients, MR showed rings of decreased signal intensity surrounding hyperintense areas that gave a target-like appearance to the globi pallidi, a finding that corresponds with the known pathologic lesions in the disease. MR reflects the metabolic and anatomic evaluation of this disease.
Ambrosetto
P
P
Department of Neuroradiology, Medical School, University of Bologna, Italy.
Nonni
R
R
Bacci
A
A
Gobbi
G
G
D005260:Female; D005917:Globus Pallidus / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D006211:Pantothenate Kinase-Associated Neurodegeneration / Q000175:diagnosis / Q000235:genetics* / Q000473:pathology