title: Abnormal lysosomal cathepsin activities in leukocytes and cultured skin fibroblasts in late infantile, but not in juvenile neuronal ceroid-lipofuscinosis (Batten disease).
authors.affiliation: Department of Pediatrics, Children's Hospital of Philadelphia.
authors.forename: M J
authors.initials: MJ
authors.lastname: Bennett
authors.forename: L
authors.initials: L
authors.lastname: Chern
authors.forename: K H
authors.initials: KH
authors.lastname: Carpenter
authors.forename: J T
authors.initials: JT
authors.lastname: Sladky
mesh_terms: D002401:Cathepsin B / Q000032:analysis*; D056655:Cathepsin H; D056668:Cathepsin L; D002403:Cathepsins / Q000032:analysis*; D002648:Child; D002675:Child, Preschool; D003546:Cysteine Endopeptidases; D010450:Endopeptidases; D005260:Female; D005347:Fibroblasts / Q000201:enzymology; D006801:Humans; D007962:Leukocytes / Q000201:enzymology; D008247:Lysosomes / Q000201:enzymology*; D009472:Neuronal Ceroid-Lipofuscinoses / Q000097:blood / Q000145:classification / Q000201:enzymology*; D012867:Skin
chemical_list: D002403:Cathepsins; D010450:Endopeptidases; D003546:Cysteine Endopeptidases; D002401:Cathepsin B; C534281:CTSL protein, human; D056668:Cathepsin L; C534126:CTSH protein, human; D056655:Cathepsin H