Early epileptic encephalopathy with suppression bursts and olivary-dentate dysplasia.
A case of neonatal epileptic encephalopathy with suppression-bursts associated with olivary dentate nuclei dysplasia is reported. This unusual association shows that the so-called Ohtahara syndrome could correspond to several different brain malformations sometimes disclosable only by neuropathological examination.
Robain
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O
Service de Neuropédiatrie, Hôpital Saint Vincent de Paul, Paris, France.
Dulac
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O
D002529:Cerebellar Nuclei / Q000473:pathology / Q000503:physiopathology*; D004292:Dominance, Cerebral / Q000502:physiology; D004569:Electroencephalography; D005071:Evoked Potentials / Q000502:physiology; D005260:Female; D006801:Humans; D007223:Infant; D009847:Olivary Nucleus / Q000473:pathology / Q000503:physiopathology*; D013036:Spasms, Infantile / Q000473:pathology / Q000503:physiopathology*