[Dopa-sensitive muscular dystonia. Segawa's syndrome. A case report].
A four-year-old girl developed difficulty in walking due to dystonia of the right then left foot, rest tremor in both hands, and rigidity. These symptoms worsened upon exertion and in the evening and were remarkably responsive to L. dopa, suggesting the diagnosis of fluctuating muscular dystonia or Segawa syndrome.
Giroud
M
M
Service de Neurologie, Hôpital Général, Dijon.
Septien
L
L
Couillault
G
G
Gras
P
P
Nivelon
J L
JL
Dumas
R
R
D002675:Child, Preschool; D003937:Diagnosis, Differential; D004421:Dystonia / Q000175:diagnosis / Q000188:drug therapy* / Q000503:physiopathology; D005260:Female; D006801:Humans; D007980:Levodopa / Q000494:pharmacology / Q000627:therapeutic use*
D007980:Levodopa
Dystonie musculaire dopa-sensible. Syndrome de Segawa. A propos d'un cas.